检索结果 - András Rab

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  1. 1
    Robust Stimulation of W1282X-CFTR Channel Activity by a Combination of Allosteric Modulators

    Robust Stimulation of W1282X-CFTR Channel Activity by a Combination of Allosteric Modulators 由 Wei Wang, Jeong S. Hong, András Rab, Eric J. Sorscher, Kevin L. Kirk

    出版 2016
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  2. 2
    Cigarette smoke and CFTR: implications in the pathogenesis of COPD

    Cigarette smoke and CFTR: implications in the pathogenesis of COPD 由 András Rab, Steven M. Rowe, S. Vamsee Raju, Zsuzsa Bebők, Sadis Matalon, James F. Collawn

    出版 2013
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  3. 3
    Activation of the Unfolded Protein Response by ΔF508 CFTR

    Activation of the Unfolded Protein Response by ΔF508 CFTR 由 Rafał Bartoszewski, András Rab, Asta Jurkuvenaite, Marina Mazur, John Wakefield, James F. Collawn, Zsuzsa Bebők

    出版 2008
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  4. 4
    Restoration of W1282X CFTR Activity by Enhanced Expression

    Restoration of W1282X CFTR Activity by Enhanced Expression 由 Steven M. Rowe, K Varga, András Rab, Zsuzsa Bebők, Kevin Byram, Yao Li, Eric J. Sorscher, John P. Clancy

    出版 2007
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  5. 5
    The Mechanism of Cystic Fibrosis Transmembrane Conductance Regulator Transcriptional Repression during the Unfolded Protein Response

    The Mechanism of Cystic Fibrosis Transmembrane Conductance Regulator Transcriptional Repression during the Unfolded Protein Response 由 Rafał Bartoszewski, András Rab, George B. Twitty, Lauren Stevenson, James A. Fortenberry, Arkadiusz Piotrowski, Jan P. Dumanski, Zsuzsa Bebők

    出版 2008
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  6. 6
    The Unfolded Protein Response (UPR)-activated Transcription Factor X-box-binding Protein 1 (XBP1) Induces MicroRNA-346 Expression That Targets the Human Antigen Peptide Transporter 1 (TAP1) mRNA and Governs Immune Regulatory Genes

    The Unfolded Protein Response (UPR)-activated Transcription Factor X-box-binding Protein 1 (XBP1) Induces MicroRNA-346 Expression That Targets the Human Antigen Peptide Transporter... 由 Rafał Bartoszewski, Joseph W. Brewer, András Rab, David K. Crossman, Sylwia Bartoszewska, Niren Kapoor, Cathy M. Fuller, James F. Collawn, Zsuzsa Bebők

    出版 2011
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  7. 7
    Elexacaftor/VX-445–mediated CFTR interactome remodeling reveals differential correction driven by mutation-specific translational dynamics

    Elexacaftor/VX-445–mediated CFTR interactome remodeling reveals differential correction driven by mutation-specific translational dynamics 由 Minsoo Kim, Eli Fritz McDonald, Carleen Mae P. Sabusap, Bibek Timalsina, Disha Joshi, Jeong S. Hong, András Rab, Eric J. Sorscher, Lars Plate

    出版 2023
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  8. 8
    Translation velocity determines the efficacy of engineered suppressor tRNAs on pathogenic nonsense mutations

    Translation velocity determines the efficacy of engineered suppressor tRNAs on pathogenic nonsense mutations 由 Nikhil Bharti, Leonardo Santos, Marcos Davyt, Stine Behrmann, Marie Eichholtz, Alejandro Jiménez‐Sánchez, Jeong S. Hong, András Rab, Eric J. Sorscher, Suki Albers, Zoya Ignatova

    出版 2024
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  9. 9
    The silent codon change I507‐ATC→ATT contributes to the severity of the ΔF508 CFTR channel dysfunction

    The silent codon change I507‐ATC→ATT contributes to the severity of the ΔF508 CFTR channel dysfunction 由 Ahmed Lazrak, Lianwu Fu, Vedrana Bali, Rafał Bartoszewski, András Rab, Viktória Havasi, Steve Keiles, John C. Kappes, Ranjit Kumar, Elliot J. Lefkowitz, Eric J. Sorscher, Sadis Matalon, James F. Collawn, Zsuzsanna Bebök

    出版 2013
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  10. 10
    Chymase Mediates Injury and Mitochondrial Damage in Cardiomyocytes during Acute Ischemia/Reperfusion in the Dog

    Chymase Mediates Injury and Mitochondrial Damage in Cardiomyocytes during Acute Ischemia/Reperfusion in the Dog 由 Junying Zheng, Chih‐Chang Wei, Naoki Hase, Ke Shi, Cheryl R. Killingsworth, Silvio Litovsky, Pamela C. Powell, Tsunefumi Kobayashi, Carlos M. Ferrario, András Rab, Inmaculada Aban, James F. Collawn, Louis J. Dell’Italia

    出版 2014
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  11. 11
    Residual function of cystic fibrosis mutants predicts response to small molecule CFTR modulators

    Residual function of cystic fibrosis mutants predicts response to small molecule CFTR modulators 由 Sangwoo T. Han, András Rab, Matthew J. Pellicore, Emily F. Davis-Marcisak, Allison F. McCague, Taylor A. Evans, Anya T. Joynt, Zhongzhou Lu, Zhiwei Cai, Karen S. Raraigh, Jeong S. Hong, David N. Sheppard, Eric J. Sorscher, Garry R. Cutting

    出版 2018
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  12. 12
    Slowing ribosome velocity restores folding and function of mutant CFTR

    Slowing ribosome velocity restores folding and function of mutant CFTR 由 Kathryn E. Oliver, Robert Rauscher, Marjolein Mijnders, Wei Wang, Matthew J. Wolpert, Jessica Maya, Carleen Mae P. Sabusap, Robert A. Kesterson, Kevin L. Kirk, András Rab, Ineke Braakman, Jeong S. Hong, John L. Hartman, Zoya Ignatova, Eric J. Sorscher

    出版 2019
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  13. 13
    Evaluating elexacaftor/tezacaftor/ivacaftor (ETI; Trikafta™) for treatment of patients with non-cystic fibrosis bronchiectasis (NCFBE): A clinical study protocol

    Evaluating elexacaftor/tezacaftor/ivacaftor (ETI; Trikafta™) for treatment of patients with non-cystic fibrosis bronchiectasis (NCFBE): A clinical study protocol 由 Colin E. Swenson, William R. Hunt, Candela Manfredi, Diana J. Beltran, Jeong S. Hong, Brian R. Davis, Shingo Suzuki, C. Barillà, András Rab, Cynthia Chico, Joy Dangerfield, Ashleigh Streby, Erin E. Barton, Elizabeth M. Cox, Arlene A. Stecenko, Adrianna Westbrook, Rebecca Kapolka, Eric J. Sorscher

    出版 2025
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  14. 14
    Derivation of Airway Basal Stem Cells from Human Pluripotent Stem Cells

    Derivation of Airway Basal Stem Cells from Human Pluripotent Stem Cells 由 Finn Hawkins, Shingo Suzuki, Mary Lou Beermann, C. Barillà, Ruobing Wang, Carlos Villacorta-Martín, Andrew Berical, J.C. Jean, Jake Le Suer, Taylor Matte, Chantelle Simone-Roach, Yang Tang, Thorsten M. Schlaeger, Ana M. Crane, Nadine Matthias, Sarah X.L. Huang, Scott H. Randell, Joshua H. Wu, Jason R. Spence, Gianni Carraro, Barry R. Stripp, András Rab, Eric J. Sorsher, Amjad Horani, Steven L. Brody, Brian R. Davis, Darrell N. Kotton

    出版 2020
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  15. 15
    A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion

    A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion 由 Jyoti Sharma, Ming Du, Eric C. Wong, Venkateshwar Mutyam, Yao Li, Jianguo Chen, Jamie R Wangen, K. Thrasher, Lianwu Fu, Ning Peng, Liping Tang, Kaimao Liu, Bini Mathew, Robert Bostwick, Corinne E. Augelli‐Szafran, Hermann Bihler, Feng Liang, Jérôme Mahiou, Josef Saltz, András Rab, Jeong S. Hong, Eric J. Sorscher, Eric M. Mendenhall, Candice J. Coppola, Kim M. Keeling, Rachel Green, Martin Mense, Mark J. Suto, Steven M. Rowe, David M. Bedwell

    出版 2021
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