نتائج البحث

Nuclear retention of full-length HTT RNA is mediated by splicing factors MBNL1 and U2AF65 حسب Xin Sun, Pan P. Li, Shanshan Zhu, Rachael Cohen, Leonard O. Marque, Christopher A. Ross, Stefan M. Pulst, Ho Yin Edwin Chan, Russell L. Margolis, Dobrila D. Rudnicki

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Suppression of Somatic Expansion Delays the Onset of Pathophysiology in a Mouse Model of Huntington’s Disease حسب Helen Budworth, Faye R. Harris, Paul D. Williams, Do Yup Lee, Amy Holt, Jens Pahnke, Bartosz Szczesny, Karina Acevedo‐Torres, Sylvette Ayala‐Peña, Cynthia T. McMurray

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Inhibition of Aggregation of Mutant Huntingtin by Nucleic Acid Aptamers In Vitro and in a Yeast Model of Huntington's Disease حسب Rajeev K. Chaudhary, Kinjal A. Patel, M. Patel, Radha H Joshi, Ipsita Roy

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HDAC6 inhibition induces mitochondrial fusion, autophagic flux and reduces diffuse mutant huntingtin in striatal neurons حسب Pedro Guedes-Dias, João de Proença, Tânia R. Soares, Ana Leitão-Rocha, Brígida R. Pinho, Michael R. Duchen, Jorge M.A. Oliveira

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Huntington’s disease: degradation of mutant huntingtin by autophagy حسب Sovan Sarkar, David C. Rubinsztein

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Huntingtin: Here, There, Everywhere! حسب Cristovao Marques Sousa, Sandrine Humbert

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PPARGC1A/PGC-1α, TFEB and enhanced proteostasis in Huntington disease حسب Albert R. La Spada

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Nature and cause of mitochondrial dysfunction in Huntington’s disease: focusing on huntingtin and the striatum حسب Jorge M.A. Oliveira

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Purkinje Cell Expression of a Mutant Allele of<i>SCA1</i>in Transgenic Mice Leads to Disparate Effects on Motor Behaviors, Followed by a Progressive Cerebellar Dysfunction and Hist... حسب H. Brent Clark, Eric N. Burright, Wael S. Yunis, Seth Larson, Claire Wilcox, Boyd K. Hartman, Antoni Matilla‐Dueñas, Huda Y. Zoghbi, Harry T. Orr

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The choreography of neuroinflammation in Huntington's disease حسب Andrea Crotti, Christopher K. Glass

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Elucidating the role of the A_2Aadenosine receptor in neurodegeneration using neurons derived from Huntington's disease iPSCs حسب Feng‐Lan Chiu, Jun-Tasi Lin, Ching-Yu Chuang, Ting Chien, Chiung‐Mei Chen, Kai‐Hsiang Chen, Han‐Yun Hsiao, Yow‐Sien Lin, Yijuang Chern, Hung‐Chih Kuo

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Purification of neuronal inclusions of patients with Huntington's disease reveals a broad range of N‐terminal fragments of expanded huntingtin and insoluble polymers حسب Guylaine Hoffner, Marie‐Laure Island, Philippe Djian

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Interaction of Huntingtin-Associated Protein with Dynactin P150^Glued حسب Shihua Li, Claire-Anne Gutekunst, Steven M. Hersch, Xiao-Jiang Li

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Impaired α-Amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid (AMPA) Receptor Trafficking and Function by Mutant Huntingtin حسب Madhuchhanda Mandal, Wei Jing, Ping Zhong, Jia Cheng, Lara J. Duffney, Wenhua Liu, Eunice Y. Yuen, Alison E. Twelvetrees, Shihua Li, Xiao‐Jiang Li, Josef T. Kittler, Zhen Yan

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Mutant Huntingtin Causes Context-Dependent Neurodegeneration in Mice with Huntington's Disease حسب Zhao-Xue Yu, Shihua Li, Joy Evans, Ajay Pillarisetti, Li He, Xiao‐Jiang Li

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<i>Dictyostelium discoideum</i> has a highly Q/N-rich proteome and shows an unusual resilience to protein aggregation حسب Liliana Malinovska, Sandra Palm, Kimberley Gibson, Jean‐Marc Verbavatz, Simon Alberti

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Machado–Joseph disease/spinocerebellar ataxia type 3 حسب Henry L. Paulson

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Chaperone Suppression of Cellular Toxicity of Huntingtin Is Independent of Polyglutamine Aggregation حسب Hui Zhou, Shihua Li, Xiao‐Jiang Li

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Ubiquitin–proteasome system involvement in Huntington’s disease حسب Zaira Ortega, José J. Lucas

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The role of dopamine in motor symptoms in the R6/2 transgenic mouse model of Huntington's disease حسب Miriam A. Hickey, Gavin P. Reynolds, A. Jennifer Morton

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