Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Background: Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingoli...

Whakaahuatanga katoa

I tiakina i:
Ngā taipitopito rārangi puna kōrero
Ngā kaituhi matua: Sabrina Nordin, Rebecca Kozor, Ravi Vijapurapu, João B. Augusto, Kristopher Knott, Gabriella Captur, Thomas A. Treibel, Uma Ramaswami, Michel Tchan, Tarekegn Geberhiwot, Richard P. Steeds, Derralynn Hughes, James Moon
Hōputu: Artigo
Reo:Ingarihi
I whakaputaina: 2019
Urunga tuihono:https://doi.org/10.1161/circimaging.119.009430
https://www.ahajournals.org/doi/pdf/10.1161/CIRCIMAGING.119.009430
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Ipurangi

https://doi.org/10.1161/circimaging.119.009430
https://www.ahajournals.org/doi/pdf/10.1161/CIRCIMAGING.119.009430

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