Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy
Background: Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingoli...
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Autori principali: | , , , , , , , , , , , , |
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Natura: | Artigo |
Lingua: | inglese |
Pubblicazione: |
2019
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Accesso online: | https://doi.org/10.1161/circimaging.119.009430 https://www.ahajournals.org/doi/pdf/10.1161/CIRCIMAGING.119.009430 |
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