Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Background: Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingoli...

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Bibliografiske detaljer
Main Authors: Sabrina Nordin, Rebecca Kozor, Ravi Vijapurapu, João B. Augusto, Kristopher Knott, Gabriella Captur, Thomas A. Treibel, Uma Ramaswami, Michel Tchan, Tarekegn Geberhiwot, Richard P. Steeds, Derralynn Hughes, James Moon
Format: Artigo
Sprog:engelsk
Udgivet: 2019
Online adgang:https://doi.org/10.1161/circimaging.119.009430
https://www.ahajournals.org/doi/pdf/10.1161/CIRCIMAGING.119.009430
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