Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Myocardial Storage, Inflammation, and Cardiac Phenotype in Fabry Disease After One Year of Enzyme Replacement Therapy

Background: Cardiac response to enzyme replacement therapy (ERT) in Fabry disease is typically assessed by measuring left ventricular mass index using echocardiography or cardiovascular magnetic resonance, but neither quantifies myocardial biology. Low native T1 in Fabry disease represents sphingoli...

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書誌詳細
主要な著者:	Sabrina Nordin, Rebecca Kozor, Ravi Vijapurapu, João B. Augusto, Kristopher Knott, Gabriella Captur, Thomas A. Treibel, Uma Ramaswami, Michel Tchan, Tarekegn Geberhiwot, Richard P. Steeds, Derralynn Hughes, James Moon
フォーマット:	Artigo
言語:	英語
出版事項:	2019
オンライン･アクセス:	https://doi.org/10.1161/circimaging.119.009430 https://www.ahajournals.org/doi/pdf/10.1161/CIRCIMAGING.119.009430
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