Efficacy of Baricitinib in the Treatment of Chilblains Associated With Aicardi‐Goutières Syndrome, a Type I Interferonopathy

Aicardi-Goutières syndrome (AGS) is a rare, juvenile-onset autoinflammatory disease characterized by basal ganglia calcification, chronic cerebrospinal fluid (CSF) lymphocytosis, and elevated type I interferon (IFN) levels in the CSF 1, 2. Typical clinical manifestations include developmental delay,...

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Main Authors: Kornvalee Meesilpavikkai, Willem A. Dik, Benjamin Schrijver, Cornelia G van Helden-Meeuwsen, Marjan A. Versnel, P. Martin van Hagen, Emilia K. Bijlsma, Claudia Ruivenkamp, Margreet J. Oele, Virgil A. S. H. Dalm
Formato: Artigo
Idioma:inglés
Publicado: 2019
Acceso en liña:https://doi.org/10.1002/art.40805
https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/art.40805
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