Loss-of-Function <i>ABCC8</i> Mutations in Pulmonary Arterial Hypertension

Loss-of-Function <i>ABCC8</i> Mutations in Pulmonary Arterial Hypertension

Background: In pulmonary arterial hypertension (PAH), pathological changes in pulmonary arterioles progressively raise pulmonary artery pressure and increase pulmonary vascular resistance, leading to right heart failure and high mortality rates. Recently, the first potassium channelopathy in PAH, be...

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Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид:	Michael S. Bohnen, Lijiang Ma, Na Zhu, Hongjian Qi, Conor McClenaghan, Claudia Gonzaga‐Jauregui, Frederick E. Dewey, John D. Overton, Jeffrey G. Reid, Alan R. Shuldiner, Aris Baras, Kevin J. Sampson, Marta Bleda, Charaka Hadinnapola, Matthias Haimel, Harm Jan Bogaard, Colin Church, Gerry Coghlan, Paul A. Corris, Mélanie Eyries, J. Simon R. Gibbs, Barbara Girerd, Arjan C. Houweling, Marc Humbert, Christophe Guignabert, David G. Kiely, Allan Lawrie, Rob V. Mackenzie Ross, Jennifer M. Martin, David Montani, Andrew J. Peacock, Joanna Pepke‐Żaba, Florent Soubrier, Jay Suntharalingam, Mark Toshner, Carmen Treacy, Richard C. Trembath, Anton Vonk Noordegraaf, John Wharton, Martin R. Wilkins, Stephen J. Wort, Katherine Yates, Stefan Gräf, Nicholas W. Morrell, Usha Krishnan, Erika B. Rosenzweig, Yufeng Shen, Colin G. Nichols, Robert S. Kass, Wendy K. Chung
Формат:	Artigo
Хэл сонгох:	англи
Хэвлэсэн:	2018
Онлайн хандалт:	https://doi.org/10.1161/circgen.118.002087
Шошгууд:	Шошго нэмэх Шошго байхгүй, Энэхүү баримтыг шошголох эхний хүн болох!

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