Ngā hua rapu - Sven W. Sauer
- E whakaatu ana i te 1 - 19 hua o te 19
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Glutaric aciduria type I and methylmalonic aciduria: Simulation of cerebral import and export of accumulating neurotoxic dicarboxylic acids in in vitro models of the blood–brain ba... mā Sven W. Sauer, Silvana Opp, Anne Mahringer, Marcin M. Kamiński, Christian Thiel, Jürgen G. Okun, Gert Fricker, Marina A. Morath, Stefan Kölker
I whakaputaina 2010Artigo -
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Neurodegeneration in Methylmalonic Aciduria Involves Inhibition of Complex II and the Tricarboxylic Acid Cycle, and Synergistically Acting Excitotoxicity mā Jürgen G. Okun, Friederike Hörster, Lilla Farkas, Patrik Feyh, Angela Hinz, Sven W. Sauer, Georg F. Hoffmann, Klaus Unsicker, Ertan Mayatepek, Stefan Kölker
I whakaputaina 2002Artigo -
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T cell Activation Is Driven by an ADP-Dependent Glucokinase Linking Enhanced Glycolysis with Mitochondrial Reactive Oxygen Species Generation mā Marcin M. Kamiński, Sven W. Sauer, Marian Kamiński, Silvana Opp, Thorsten Ruppert, Paulius Grigaravičius, P. Grudnik, Hermann-Josef Gröne, Peter H. Krammer, Karsten Gülow
I whakaputaina 2012Artigo -
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Methylmalonic Acid, a Biochemical Hallmark of Methylmalonic Acidurias but No Inhibitor of Mitochondrial Respiratory Chain mā Stefan Kölker, Marina A. Schwab, Friederike Hörster, Sven W. Sauer, Angela Hinz, Nicole I. Wolf, Ertan Mayatepek, Georg F. Hoffmann, Jan Smeitink, Jürgen G. Okun
I whakaputaina 2003Artigo -
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Secondary mitochondrial dysfunction in propionic aciduria: a pathogenic role for endogenous mitochondrial toxins mā Marina A. Schwab, Sven W. Sauer, Jürgen G. Okun, Leo Nijtmans, Richard J. Rodenburg, Lambert P. van den Heuvel, Stefan Dröse, Ulrich Brandt, Georg F. Hoffmann, H. ter Laak, Stefan Kölker, Jan Smeitink
I whakaputaina 2006Artigo -
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DHTKD1 Mutations Cause 2-Aminoadipic and 2-Oxoadipic Aciduria mā Katharina Danhauser, Sven W. Sauer, Tobias B. Haack, Thomas Wieland, Christian Staufner, Elisabeth Graf, Johannes Zschocke, Tim M. Strom, Thorsten Traub, Jürgen G. Okun, Thomas Meitinger, Georg F. Hoffmann, Holger Prokisch, Stefan Kölker
I whakaputaina 2012Artigo -
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The HMGB1 protein induces a metabolic type of tumour cell death by blocking aerobic respiration mā Georg Gdynia, Sven W. Sauer, Jürgen Kopitz, Dominik Fuchs, Katarina Duglova, Thorsten Ruppert, Matthias Miller, Jens Pahl, Adelheid Cerwenka, Markus Enders, Heimo Mairbäurl, Marcin M. Kamiński, Roland Penzel, Christine Zhang, Jonathan C. Fuller, Rebecca C. Wade, Axel Benner, Jenny C. Chang, Hermann Brenner, Michael Hoffmeister, Hanswalter Zentgraf, Peter Schirmacher, Wilfried Roth
I whakaputaina 2016Artigo -
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Inhibition of Endothelial Notch Signaling Impairs Fatty Acid Transport and Leads to Metabolic and Vascular Remodeling of the Adult Heart mā Markus Jabs, Adam J. Rose, Lorenz Lehmann, Jacqueline Taylor, Iris Moll, Tjeerd Sijmonsma, Stefanie E. Herberich, Sven W. Sauer, Gernot Poschet, Giuseppina Federico, Carolin Mogler, Eva‐Maria Weis, Hellmut G. Augustin, Minhong Yan, Norbert Gretz, Roland M. Schmid, Ralf H. Adams, Hermann-Joseph Gröne, Rüdiger Hell, Jürgen G. Okun, Johannes Backs, Peter P. Nawroth, Stephan Herzig, Andreas Fischer
I whakaputaina 2018Artigo -
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The lipid-droplet-associated protein ABHD5 protects the heart through proteolysis of HDAC4 mā Zegeye Hailu Jebessa, Kumar D. Shanmukha, Matthias Dewenter, Lorenz Lehmann, Chang Xu, Friederike Schreiter, Dominik Siede, Xue-Min Gong, Barbara C. Worst, Giuseppina Federico, Sven W. Sauer, Tamás Fischer, Lisa Wechselberger, Oliver J. Müller, Samuel Sossalla, Christoph Dieterich, Patrick Most, Herrmann‐Josef Gröne, Cédric Moro, Monika Oberer, Guenter Haemmerle, Hugo A. Katus, Jens Tyedmers, Johannes Backs
I whakaputaina 2019Artigo -
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Biallelic IARS Mutations Cause Growth Retardation with Prenatal Onset, Intellectual Disability, Muscular Hypotonia, and Infantile Hepatopathy mā Robert Kopajtich, Kei Murayama, Andreas Janecke, Tobias B. Haack, Maximilian Breuer, A. S. Knisely, Inga Harting, Toya Ohashi, Yasushi Okazaki, Daisaku WATANABE, Yoshimi Tokuzawa, Urania Kotzaeridou, Stefan Kölker, Sven W. Sauer, Michael Carl, Simon Straub, Andreas Entenmann, Elke R. Gizewski, René G. Feichtinger, Johannes A. Mayr, K. Lackner, Tim M. Strom, Thomas Meitinger, Thomas Müller, Akira Ohtake, Georg F. Hoffmann, Holger Prokisch, Christian Staufner
I whakaputaina 2016Artigo -
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A non‐enzymatic function of 17β‐hydroxysteroid dehydrogenase type 10 is required for mitochondrial integrity and cell survival mā Katharina Rauschenberger, Katja Schöler, Jörn Oliver Sass, Sven W. Sauer, Zdenka Djuric, Cordula Rumig, Nicole I. Wolf, Jürgen G. Okun, Stefan Kölker, Heinz Schwarz, Christine Fischer, Beate Grziwa, Heiko Runz, Astrid Nümann, N. Shafqat, K.L. Kavanagh, Günter J. Hämmerling, Ronald J. A. Wanders, Julian Hamilton‐Shield, U. Wendel, David M. Stern, Peter P. Nawroth, Georg F. Hoffmann, Claus R. Bartram, Bernd Arnold, Angelika Bierhaus, Udo Oppermann, Herbert Steinbeißer, Johannes Zschocke
I whakaputaina 2010Artigo
Ngā utauta rapu:
Ngā marau whai pānga
Biology
Biochemistry
Cell biology
Enzyme
Chemistry
Mitochondrion
Endocrinology
Gene
Medicine
Internal medicine
Genetics
Metabolism
Receptor
Respiratory chain
Citric acid cycle
Glycolysis
Mitochondrial ROS
Mitochondrial respiratory chain
Oxidative phosphorylation
Reactive oxygen species
Amino acid
Anaerobic glycolysis
Bioenergetics
Cytosol
Dehydrogenase
Function (biology)
Glutaric acid
Messenger RNA
Methylmalonic acid
Oxidative stress