Search Results - Sandrine Arbogast
- Showing 1 - 10 results of 10
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Muscle strength, quantity and quality and muscle fat quantity and their association with oxidative stress in patients with facioscapulohumeral muscular dystrophy: Effect of antioxi... by Vinicius Dias Wilson, Sébastien Bommart, Emilie Passerieux, Claire Thomas, Joël Pincemaïl, Marie Picot, Jacques Mercier, Florence Portet, Sandrine Arbogast, Dalila Laoudj‐Chenivesse
Published 2024Artigo -
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A mutation in the<i>SEPN1</i>selenocysteine redefinition element (SRE) reduces selenocysteine incorporation and leads to<i>SEPN1</i>-related myopathy by Baijayanta Maiti, Sandrine Arbogast, Val��rie Allamand, Mark W. Moyle, Christine B. Anderson, Pascale Richard, Pascale Guicheney, Ana Ferreiro, Kevin M. Flanigan, Michael Howard
Published 2008Artigo -
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Nutritional Status of Patients with Facioscapulohumeral Muscular Dystrophy by Sedda Amzali, Vinicius Dias Wilson, Sébastien Bommart, Marie‐Christine Picot, Simon Galas, Jacques Mercier, Patrick Poucheret, Jean‐Paul Cristol, Sandrine Arbogast, Dalila Laoudj‐Chenivesse
Published 2023Artigo -
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Increased Muscle Stress-Sensitivity Induced by Selenoprotein N Inactivation in Mouse: A Mammalian Model for SEPN1-Related Myopathy by Mathieu Rederstorff, Perrine Castets, Sandrine Arbogast, Jeanne Lainé, Stéphane Vassilopoulos, Maud Beuvin, O. Dubourg, Alban Vignaud, Arnaud Ferry, Alain Krol, Valérie Allamand, Pascale Guicheney, Ana Ferreiro, Alain Lescure
Published 2011Artigo -
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Oxidative stress and successful antioxidant treatment in models of RYR1-related myopathy by James J. Dowling, Sandrine Arbogast, Junguk Hur, Darcee D. Nelson, Anna McEvoy, Trent A. Waugh, Isabelle Marty, Joël Lunardi, Susan V. Brooks, John Y. Kuwada, Ana Ferreiro
Published 2012Artigo -
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Impaired oxygen demand during exercise is related to oxidative stress and muscle function in Facioscapulohumeral Muscular Dystrophy by Vinicius Dias Wilson, Claire Thomas, Emilie Passerieux, Gérald Hugon, Fabien Pillard, André Gustavo Pereira de Andrade, Sébastien Bommart, Marie‐Christine Picot, Joël Pincemaïl, Jacques Mercier, Sandrine Arbogast, Dalila Laoudj‐Chenivesse
Published 2018Artigo -
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CLOCK and BMAL1 regulate <i>MyoD</i> and are necessary for maintenance of skeletal muscle phenotype and function by Jessica L. Andrews, Xiping Zhang, John J. McCarthy, Erin L. McDearmon, Troy A. Hornberger, Brenda Russell, Kenneth S. Campbell, Sandrine Arbogast, Michael B. Reid, J. Walker, John B. Hogenesch, Joseph S. Takahashi, Karyn A. Esser
Published 2010Artigo -
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Defective endoplasmic reticulum-mitochondria contacts and bioenergetics in SEPN1-related myopathy by Anne Filipe, Alexander Chernorudskiy, Sandrine Arbogast, Ersilia Varone, Rocío-Nur Villar-Quiles, Diego Pozzer, Maryline Moulin, Stefano Fumagalli, Éva Cabet, Swati Dudhal, Maria Grazia De Simoni, R Denis, Nathalie Vadrot, C. Dill, Matteo Giovarelli, Luke I. Szweda, Clara De Palma, Paolo Pinton, Carlotta Giorgi, Carlo Viscomi, Emilio Clementi, Sonia Missiroli, Simona Boncompagni, Ester Zito, Ana Ferreiro
Published 2020Artigo
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Biology
Internal medicine
Medicine
Chemistry
Biochemistry
Endocrinology
Oxidative stress
Myopathy
Skeletal muscle
Cell biology
Facioscapulohumeral muscular dystrophy
Muscular dystrophy
Gene
Genetics
Myocyte
Myogenesis
Oxidative phosphorylation
Antioxidant
Atrophy
Bioenergetics
Biopsy
CLOCK
Calcium
Calcium signaling
Cardiology
Circadian clock
Circadian rhythm
Congenital myopathy
Cysteine
Endoplasmic reticulum