Torthaí cuardaigh - Rubén Quintana–Cabrera
- 1 - 12 toradh as 12 á dtaispeáint
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1
Determinants and outcomes of mitochondrial dynamics de réir Rubén Quintana–Cabrera, Luca Scorrano
Foilsithe / Cruthaithe 2023Revisão -
2
Opa1 relies on cristae preservation and ATP synthase to curtail reactive oxygen species accumulation in mitochondria de réir Rubén Quintana–Cabrera, Israel Manjarrés-Raza, Carlos Vicente‐Gutiérrez, Mauro Corrado, Juan P. Bolaños, Luca Scorrano
Foilsithe / Cruthaithe 2021Artigo -
3
γ-Glutamylcysteine detoxifies reactive oxygen species by acting as glutathione peroxidase-1 cofactor de réir Rubén Quintana–Cabrera, Seila Fernández-Fernández, Verónica Bobo-Jiménez, Javier Escobar, Juan Sastre, Ángeles Almeida, Juan P. Bolaños
Foilsithe / Cruthaithe 2012Artigo -
4
Dysfunctional mitochondria accumulate in a skeletal muscle knockout model of Smn1, the causal gene of spinal muscular atrophy de réir Francesco Chemello, Michela Pozzobon, Lorenza Iolanda Tsansizi, Tatiana Varanita, Rubén Quintana–Cabrera, Daniele Bonesso, Martina Piccoli, Gerolamo Lanfranchi, Marta Giacomello, Luca Scorrano, Camilla Bean
Foilsithe / Cruthaithe 2023Artigo -
5
Early effects of the antineoplastic agent salinomycin on mitochondrial function de réir Antonella Managò, Luigi Leanza, Luca Carraretto, Nadia Sassi, Silvia Grancara, Rubén Quintana–Cabrera, Valentina Trimarco, Antonio Toninello, Luca Scorrano, Livio Trentin, Gianpietro Semenzato, Erich Gulbins, Mario Zoratti, Ildikò Szabó
Foilsithe / Cruthaithe 2015Artigo -
6
The cristae modulator Optic atrophy 1 requires mitochondrial ATP synthase oligomers to safeguard mitochondrial function de réir Rubén Quintana–Cabrera, Charlotte Quirin, Christina Glytsou, Mauro Corrado, Andrea Urbani, Anna Pellattiero, Enrique Calvo, Jesús Vázquez, José Antonio Enrı́quez, Christoph Gerle, María Eugenia Soriano, Paolo Bernardi, Luca Scorrano
Foilsithe / Cruthaithe 2018Artigo -
7
Inhibition of autophagy curtails visual loss in a model of autosomal dominant optic atrophy de réir Marta Zaninello, Konstantinos Palikaras, Déborah Naón, Keiko Iwata, Stéphanie Herkenne, Rubén Quintana–Cabrera, Martina Semenzato, Francesca Grespi, Fred N. Ross‐Cisneros, Valério Carelli, Alfredo A. Sadun, Nektarios Tavernarakis, Luca Scorrano
Foilsithe / Cruthaithe 2020Artigo -
8
The Opa1-Dependent Mitochondrial Cristae Remodeling Pathway Controls Atrophic, Apoptotic, and Ischemic Tissue Damage de réir Tatiana Varanita, María Eugenia Soriano, Vanina Romanello, Tania Zaglia, Rubén Quintana–Cabrera, Martina Semenzato, Roberta Menabò, Veronica Costa, Gabriele Civiletto, Paola Pesce, Carlo Viscomi, Massimo Zeviani, Fabio Di Lisa, Marco Mongillo, Marco Sandri, Luca Scorrano
Foilsithe / Cruthaithe 2015Artigo -
9
Mitochondrial Cristae Shape Determines Respiratory Chain Supercomplexes Assembly and Respiratory Efficiency de réir Sara Cogliati, Christian Frezza, María Eugenia Soriano, Tatiana Varanita, Rubén Quintana–Cabrera, Mauro Corrado, Sara Cipolat, Veronica Costa, Alberto Casarin, Lígia C. Gomes, Ester Perales‐Clemente, Leonardo Salviati, Patricio Fernández‐Silva, José Antonio Enrı́quez, Luca Scorrano
Foilsithe / Cruthaithe 2013Artigo -
10
MFN2 mutations in Charcot–Marie–Tooth disease alter mitochondria-associated ER membrane function but do not impair bioenergetics de réir Delfina Larrea, Marta Pera, Adriano Gonnelli, Rubén Quintana–Cabrera, Hasan O. Akman, Cristina Guardia‐Laguarta, Kevin Velasco, Estela Area‐Gómez, Federica Dal Bello, Diego De Stefani, Rita Horváth, Michael E. Shy, Eric A. Schon, Marta Giacomello
Foilsithe / Cruthaithe 2019Artigo -
11
Impaired Mitochondrial ATP Production Downregulates Wnt Signaling via ER Stress Induction de réir Roberto Costa, Roberta Peruzzo, Magdalena Bachmann, Giulia Dalla Montà, Mattia Vicario, Giulia Santinon, Andrea Mattarei, Enrico Moro, Rubén Quintana–Cabrera, Luca Scorrano, Massimo Zeviani, Francesca Vallese, Mario Zoratti, Cristina Paradisi, Francesco Argenton, Marisa Brini, Tito Calì, Sirio Dupont, Ildikò Szabó, Luigi Leanza
Foilsithe / Cruthaithe 2019Artigo -
12
Aberrant upregulation of the glycolytic enzyme PFKFB3 in CLN7 neuronal ceroid lipofuscinosis de réir Irene López-Fabuel, Marina García‐Macia, Costantina Buondelmonte, Olga Burmistrova, Nicoló Bonora, Paula Alonso-Batan, Brenda Morant-Ferrando, Carlos Vicente‐Gutiérrez, Daniel Jimenez‐Blasco, Rubén Quintana–Cabrera, Emilio Fernández, Jordi Llop, Pedro Ramos‐Cabrer, Aseel Sharaireh, Marta Guevara‐Ferrer, Lorna M. FitzPatrick, Christopher D. Thompton, Tristan R. McKay, Stephan Storch, Diego L. Medina, Sara Mole, П. О. Федичев, Ángeles Almeida, Juan P. Bolaños
Foilsithe / Cruthaithe 2022Artigo
Uirlisí cuardaigh:
Ábhair a bhaineann le hábhar
Biology
Cell biology
Mitochondrion
Gene
Biochemistry
Genetics
Mitochondrial DNA
mitochondrial fusion
Apoptosis
Chemistry
Enzyme
Anatomy
Atrophy
ATP synthase
Autophagy
Downregulation and upregulation
Endoplasmic reticulum
Function (biology)
Immunology
Pathogenesis
Phenotype
Reactive oxygen species
AMPK
ATP–ADP translocase
Adenosine triphosphate
Antibiotics
Antioxidant
Batten disease
Bioenergetics
Business