檢索結果 - Rubén Quintana–Cabrera
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Dysfunctional mitochondria accumulate in a skeletal muscle knockout model of Smn1, the causal gene of spinal muscular atrophy 由 Francesco Chemello, Michela Pozzobon, Lorenza Iolanda Tsansizi, Tatiana Varanita, Rubén Quintana–Cabrera, Daniele Bonesso, Martina Piccoli, Gerolamo Lanfranchi, Marta Giacomello, Luca Scorrano, Camilla Bean
出版 2023Artigo -
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Early effects of the antineoplastic agent salinomycin on mitochondrial function 由 Antonella Managò, Luigi Leanza, Luca Carraretto, Nadia Sassi, Silvia Grancara, Rubén Quintana–Cabrera, Valentina Trimarco, Antonio Toninello, Luca Scorrano, Livio Trentin, Gianpietro Semenzato, Erich Gulbins, Mario Zoratti, Ildikò Szabó
出版 2015Artigo -
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The cristae modulator Optic atrophy 1 requires mitochondrial ATP synthase oligomers to safeguard mitochondrial function 由 Rubén Quintana–Cabrera, Charlotte Quirin, Christina Glytsou, Mauro Corrado, Andrea Urbani, Anna Pellattiero, Enrique Calvo, Jesús Vázquez, José Antonio Enrı́quez, Christoph Gerle, María Eugenia Soriano, Paolo Bernardi, Luca Scorrano
出版 2018Artigo -
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Inhibition of autophagy curtails visual loss in a model of autosomal dominant optic atrophy 由 Marta Zaninello, Konstantinos Palikaras, Déborah Naón, Keiko Iwata, Stéphanie Herkenne, Rubén Quintana–Cabrera, Martina Semenzato, Francesca Grespi, Fred N. Ross‐Cisneros, Valério Carelli, Alfredo A. Sadun, Nektarios Tavernarakis, Luca Scorrano
出版 2020Artigo -
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The Opa1-Dependent Mitochondrial Cristae Remodeling Pathway Controls Atrophic, Apoptotic, and Ischemic Tissue Damage 由 Tatiana Varanita, María Eugenia Soriano, Vanina Romanello, Tania Zaglia, Rubén Quintana–Cabrera, Martina Semenzato, Roberta Menabò, Veronica Costa, Gabriele Civiletto, Paola Pesce, Carlo Viscomi, Massimo Zeviani, Fabio Di Lisa, Marco Mongillo, Marco Sandri, Luca Scorrano
出版 2015Artigo -
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Mitochondrial Cristae Shape Determines Respiratory Chain Supercomplexes Assembly and Respiratory Efficiency 由 Sara Cogliati, Christian Frezza, María Eugenia Soriano, Tatiana Varanita, Rubén Quintana–Cabrera, Mauro Corrado, Sara Cipolat, Veronica Costa, Alberto Casarin, Lígia C. Gomes, Ester Perales‐Clemente, Leonardo Salviati, Patricio Fernández‐Silva, José Antonio Enrı́quez, Luca Scorrano
出版 2013Artigo -
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MFN2 mutations in Charcot–Marie–Tooth disease alter mitochondria-associated ER membrane function but do not impair bioenergetics 由 Delfina Larrea, Marta Pera, Adriano Gonnelli, Rubén Quintana–Cabrera, Hasan O. Akman, Cristina Guardia‐Laguarta, Kevin Velasco, Estela Area‐Gómez, Federica Dal Bello, Diego De Stefani, Rita Horváth, Michael E. Shy, Eric A. Schon, Marta Giacomello
出版 2019Artigo -
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Impaired Mitochondrial ATP Production Downregulates Wnt Signaling via ER Stress Induction 由 Roberto Costa, Roberta Peruzzo, Magdalena Bachmann, Giulia Dalla Montà, Mattia Vicario, Giulia Santinon, Andrea Mattarei, Enrico Moro, Rubén Quintana–Cabrera, Luca Scorrano, Massimo Zeviani, Francesca Vallese, Mario Zoratti, Cristina Paradisi, Francesco Argenton, Marisa Brini, Tito Calì, Sirio Dupont, Ildikò Szabó, Luigi Leanza
出版 2019Artigo -
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Aberrant upregulation of the glycolytic enzyme PFKFB3 in CLN7 neuronal ceroid lipofuscinosis 由 Irene López-Fabuel, Marina García‐Macia, Costantina Buondelmonte, Olga Burmistrova, Nicoló Bonora, Paula Alonso-Batan, Brenda Morant-Ferrando, Carlos Vicente‐Gutiérrez, Daniel Jimenez‐Blasco, Rubén Quintana–Cabrera, Emilio Fernández, Jordi Llop, Pedro Ramos‐Cabrer, Aseel Sharaireh, Marta Guevara‐Ferrer, Lorna M. FitzPatrick, Christopher D. Thompton, Tristan R. McKay, Stephan Storch, Diego L. Medina, Sara Mole, П. О. Федичев, Ángeles Almeida, Juan P. Bolaños
出版 2022Artigo
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