Resultados da busca - Roger Sandhoff
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Very long chain sphingolipids: Tissue expression, function and synthesis por Roger Sandhoff
Publicado em 2009Revisão -
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Emerging concepts of ganglioside metabolism por Roger Sandhoff, Konrad Sandhoff
Publicado em 2018Revisão -
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Adult Ceramide Synthase 2 (CERS2)-deficient Mice Exhibit Myelin Sheath Defects, Cerebellar Degeneration, and Hepatocarcinomas por Silke Imgrund, Dieter Hartmann, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Volkmar Gieselmann, Konrad Sandhoff, Klaus Willecke
Publicado em 2009Artigo -
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Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage por Hiroki Mizukami, Yide Mi, Ryuichi Wada, Mari Kono, Tadashi Yamashita, Yujing Liu, Norbert Werth, Roger Sandhoff, Konrad Sandhoff, Richard L. Proia
Publicado em 2002Artigo -
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Depletion of ceramides with very long chain fatty acids causes defective skin permeability barrier function, and neonatal lethality in ELOVL4 deficient mice por Wenmei Li, Roger Sandhoff, Mari Kono, Patricia M. Zerfas, Vickie Hoffmann, Bryan Char-Hoa Ding, Richard L. Proia, Chu‐Xia Deng
Publicado em 2007Artigo -
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Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage por Hiroki Mizukami, Yide Mi, Ryuichi Wada, Mari Kono, Tadashi Yamashita, Yujing Liu, Norbert Werth, Roger Sandhoff, Konrad Sandhoff, Richard L. Proia
Publicado em 2002Artigo -
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1-O-acylceramides are natural components of human and mouse epidermis por Mariona Rabionet, Aline Bayerle, Christian Marsching, Richard Jennemann, Hermann-Josef Gröne, Yildiz Yildiz, Dagmar Wachten, Walter Shaw, James A. Shayman, Roger Sandhoff
Publicado em 2013Artigo -
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Diastereomer-specific quantification of bioactive hexosylceramides from bacteria and mammals por Johanna von Gerichten, Kerstin Schlosser, Dominic Lamprecht, Ivan Morace, Matthias Eckhardt, Dagmar Wachten, Richard Jennemann, Hermann-Josef Gröne, Matthias Mack, Roger Sandhoff
Publicado em 2017Artigo -
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Interruption of ganglioside synthesis produces central nervous system degeneration and altered axon–glial interactions por Tadashi Yamashita, Yunping Wu, Roger Sandhoff, Norbert Werth, Hiroki Mizukami, Jessica M. Ellis, Jeffrey L. Dupree, Rudolf Geyer, Konrad Sandhoff, Richard L. Proia
Publicado em 2005Artigo -
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Accumulation of Glucosylceramide in Murine Testis, Caused by Inhibition of β-Glucosidase 2 por Charlotte M. Walden, Roger Sandhoff, Chia‐Chen Chuang, Yildiz Yildiz, Terry D. Butters, Raymond A. Dwek, Frances M. Platt, Aarnoud C. van der Spoel
Publicado em 2007Artigo -
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Male meiotic cytokinesis requires ceramide synthase 3-dependent sphingolipids with unique membrane anchors por Mariona Rabionet, Aline Bayerle, Richard Jennemann, Hans Heid, Jens Fuchser, Christian Marsching, Štefan Porubský, Christian Bolenz, Florian Guillou, Hermann‐Josef Gröne, Karin Gorgas, Roger Sandhoff
Publicado em 2015Artigo -
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Ablation of Neuronal Ceramide Synthase 1 in Mice Decreases Ganglioside Levels and Expression of Myelin-associated Glycoprotein in Oligodendrocytes por Christina Ginkel, Dieter Hartmann, Katharina vom Dorp, Armin Zlomuzica, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Mariona Rabionet, Ekrem Dere, Peter Dörmann, Konrad Sandhoff, Klaus Willecke
Publicado em 2012Artigo -
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Electrospray Ionization Tandem Mass Spectrometry (Esi-Ms/Ms) Analysis of the Lipid Molecular Species Composition of Yeast Subcellular Membranes Reveals Acyl Chain-Based Sorting/Rem... por Roger Schneiter, Britta Brügger, Roger Sandhoff, Günther Zellnig, A. Philip Leber, Manfred Lampl, Karin Athenstaedt, Claudia Hrastnik, Sandra Eder, Günther Daum, Fritz Paltauf, Felix Wieland, Sepp D. Kohlwein
Publicado em 1999Artigo -
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Cell-specific deletion of glucosylceramide synthase in brain leads to severe neural defects after birth por Richard Jennemann, Roger Sandhoff, Shijun Wang, Éva Kiss, Norbert Gretz, Cecilia Zuliani, Ana Martín-Villalba, Richard Jäger, Hubert Schorle, Marc Kenzelmann, Mahnaz Bonrouhi, Herbert Wiegandt, Hermann-Josef Gröne
Publicado em 2005Artigo -
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Novel Class of Glycosphingolipids Involved in Male Fertility por Roger Sandhoff, Rudolf Geyer, Richard Jennemann, Claudia Paret, Éva Kiss, Tadashi Yamashita, Karin Gorgas, Tjeerd Sijmonsma, Masao Iwamori, C. Finaz, Richard L. Proia, Herbert Wiegandt, Hermann-Josef Gröne
Publicado em 2005Artigo -
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Sulfatides are required for renal adaptation to chronic metabolic acidosis por Paula Stettner, Soline Bourgeois, Christian Marsching, Milena Traykova-Brauch, Štefan Porubský, Viola Nordström, Carsten Hopf, Robert Koesters, Roger Sandhoff, Herbert Wiegandt, Carsten A. Wagner, Hermann‐Josef Gröne, Richard Jennemann
Publicado em 2013Artigo
Ferramentas de busca:
Assuntos relacionados
Biology
Biochemistry
Cell biology
Gene
Sphingolipid
Apoptosis
Ceramide
Chemistry
Endocrinology
Genetics
Medicine
Enzyme
Mutant
Immunology
Inflammation
Internal medicine
Membrane
Central nervous system
Ceramide synthase
Ganglioside
Anatomy
Disease
Endoplasmic reticulum
Glycolipid
In vitro
Barrier function
Cerebellum
Epidermis (zoology)
Germ cell
Golgi apparatus