Rezultaty - Roger Sandhoff
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Adult Ceramide Synthase 2 (CERS2)-deficient Mice Exhibit Myelin Sheath Defects, Cerebellar Degeneration, and Hepatocarcinomas od Silke Imgrund, Dieter Hartmann, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Volkmar Gieselmann, Konrad Sandhoff, Klaus Willecke
Wydane 2009Artigo -
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Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage od Hiroki Mizukami, Yide Mi, Ryuichi Wada, Mari Kono, Tadashi Yamashita, Yujing Liu, Norbert Werth, Roger Sandhoff, Konrad Sandhoff, Richard L. Proia
Wydane 2002Artigo -
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Depletion of ceramides with very long chain fatty acids causes defective skin permeability barrier function, and neonatal lethality in ELOVL4 deficient mice od Wenmei Li, Roger Sandhoff, Mari Kono, Patricia M. Zerfas, Vickie Hoffmann, Bryan Char-Hoa Ding, Richard L. Proia, Chu‐Xia Deng
Wydane 2007Artigo -
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Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage od Hiroki Mizukami, Yide Mi, Ryuichi Wada, Mari Kono, Tadashi Yamashita, Yujing Liu, Norbert Werth, Roger Sandhoff, Konrad Sandhoff, Richard L. Proia
Wydane 2002Artigo -
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1-O-acylceramides are natural components of human and mouse epidermis od Mariona Rabionet, Aline Bayerle, Christian Marsching, Richard Jennemann, Hermann-Josef Gröne, Yildiz Yildiz, Dagmar Wachten, Walter Shaw, James A. Shayman, Roger Sandhoff
Wydane 2013Artigo -
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Diastereomer-specific quantification of bioactive hexosylceramides from bacteria and mammals od Johanna von Gerichten, Kerstin Schlosser, Dominic Lamprecht, Ivan Morace, Matthias Eckhardt, Dagmar Wachten, Richard Jennemann, Hermann-Josef Gröne, Matthias Mack, Roger Sandhoff
Wydane 2017Artigo -
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Interruption of ganglioside synthesis produces central nervous system degeneration and altered axon–glial interactions od Tadashi Yamashita, Yunping Wu, Roger Sandhoff, Norbert Werth, Hiroki Mizukami, Jessica M. Ellis, Jeffrey L. Dupree, Rudolf Geyer, Konrad Sandhoff, Richard L. Proia
Wydane 2005Artigo -
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Accumulation of Glucosylceramide in Murine Testis, Caused by Inhibition of β-Glucosidase 2 od Charlotte M. Walden, Roger Sandhoff, Chia‐Chen Chuang, Yildiz Yildiz, Terry D. Butters, Raymond A. Dwek, Frances M. Platt, Aarnoud C. van der Spoel
Wydane 2007Artigo -
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Male meiotic cytokinesis requires ceramide synthase 3-dependent sphingolipids with unique membrane anchors od Mariona Rabionet, Aline Bayerle, Richard Jennemann, Hans Heid, Jens Fuchser, Christian Marsching, Štefan Porubský, Christian Bolenz, Florian Guillou, Hermann‐Josef Gröne, Karin Gorgas, Roger Sandhoff
Wydane 2015Artigo -
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Ablation of Neuronal Ceramide Synthase 1 in Mice Decreases Ganglioside Levels and Expression of Myelin-associated Glycoprotein in Oligodendrocytes od Christina Ginkel, Dieter Hartmann, Katharina vom Dorp, Armin Zlomuzica, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Mariona Rabionet, Ekrem Dere, Peter Dörmann, Konrad Sandhoff, Klaus Willecke
Wydane 2012Artigo -
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Electrospray Ionization Tandem Mass Spectrometry (Esi-Ms/Ms) Analysis of the Lipid Molecular Species Composition of Yeast Subcellular Membranes Reveals Acyl Chain-Based Sorting/Rem... od Roger Schneiter, Britta Brügger, Roger Sandhoff, Günther Zellnig, A. Philip Leber, Manfred Lampl, Karin Athenstaedt, Claudia Hrastnik, Sandra Eder, Günther Daum, Fritz Paltauf, Felix Wieland, Sepp D. Kohlwein
Wydane 1999Artigo -
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Cell-specific deletion of glucosylceramide synthase in brain leads to severe neural defects after birth od Richard Jennemann, Roger Sandhoff, Shijun Wang, Éva Kiss, Norbert Gretz, Cecilia Zuliani, Ana Martín-Villalba, Richard Jäger, Hubert Schorle, Marc Kenzelmann, Mahnaz Bonrouhi, Herbert Wiegandt, Hermann-Josef Gröne
Wydane 2005Artigo -
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Novel Class of Glycosphingolipids Involved in Male Fertility od Roger Sandhoff, Rudolf Geyer, Richard Jennemann, Claudia Paret, Éva Kiss, Tadashi Yamashita, Karin Gorgas, Tjeerd Sijmonsma, Masao Iwamori, C. Finaz, Richard L. Proia, Herbert Wiegandt, Hermann-Josef Gröne
Wydane 2005Artigo -
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Sulfatides are required for renal adaptation to chronic metabolic acidosis od Paula Stettner, Soline Bourgeois, Christian Marsching, Milena Traykova-Brauch, Štefan Porubský, Viola Nordström, Carsten Hopf, Robert Koesters, Roger Sandhoff, Herbert Wiegandt, Carsten A. Wagner, Hermann‐Josef Gröne, Richard Jennemann
Wydane 2013Artigo
Narzędzie wyszukiwania:
Podobne hasła
Biology
Biochemistry
Cell biology
Gene
Sphingolipid
Apoptosis
Ceramide
Chemistry
Endocrinology
Genetics
Medicine
Enzyme
Mutant
Immunology
Inflammation
Internal medicine
Membrane
Central nervous system
Ceramide synthase
Ganglioside
Anatomy
Disease
Endoplasmic reticulum
Glycolipid
In vitro
Barrier function
Cerebellum
Epidermis (zoology)
Germ cell
Golgi apparatus