検索結果 - Roger Sandhoff
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Very long chain sphingolipids: Tissue expression, function and synthesis 著者: Roger Sandhoff
出版事項 2009Revisão -
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Emerging concepts of ganglioside metabolism 著者: Roger Sandhoff, Konrad Sandhoff
出版事項 2018Revisão -
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Adult Ceramide Synthase 2 (CERS2)-deficient Mice Exhibit Myelin Sheath Defects, Cerebellar Degeneration, and Hepatocarcinomas 著者: Silke Imgrund, Dieter Hartmann, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Volkmar Gieselmann, Konrad Sandhoff, Klaus Willecke
出版事項 2009Artigo -
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Depletion of ceramides with very long chain fatty acids causes defective skin permeability barrier function, and neonatal lethality in ELOVL4 deficient mice 著者: Wenmei Li, Roger Sandhoff, Mari Kono, Patricia M. Zerfas, Vickie Hoffmann, Bryan Char-Hoa Ding, Richard L. Proia, Chu‐Xia Deng
出版事項 2007Artigo -
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Interruption of ganglioside synthesis produces central nervous system degeneration and altered axon–glial interactions 著者: Tadashi Yamashita, Yunping Wu, Roger Sandhoff, Norbert Werth, Hiroki Mizukami, Jessica M. Ellis, Jeffrey L. Dupree, Rudolf Geyer, Konrad Sandhoff, Richard L. Proia
出版事項 2005Artigo -
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Male meiotic cytokinesis requires ceramide synthase 3-dependent sphingolipids with unique membrane anchors 著者: Mariona Rabionet, Aline Bayerle, Richard Jennemann, Hans Heid, Jens Fuchser, Christian Marsching, Štefan Porubský, Christian Bolenz, Florian Guillou, Hermann‐Josef Gröne, Karin Gorgas, Roger Sandhoff
出版事項 2015Artigo -
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Ablation of Neuronal Ceramide Synthase 1 in Mice Decreases Ganglioside Levels and Expression of Myelin-associated Glycoprotein in Oligodendrocytes 著者: Christina Ginkel, Dieter Hartmann, Katharina vom Dorp, Armin Zlomuzica, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Mariona Rabionet, Ekrem Dere, Peter Dörmann, Konrad Sandhoff, Klaus Willecke
出版事項 2012Artigo -
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Electrospray Ionization Tandem Mass Spectrometry (Esi-Ms/Ms) Analysis of the Lipid Molecular Species Composition of Yeast Subcellular Membranes Reveals Acyl Chain-Based Sorting/Rem... 著者: Roger Schneiter, Britta Brügger, Roger Sandhoff, Günther Zellnig, A. Philip Leber, Manfred Lampl, Karin Athenstaedt, Claudia Hrastnik, Sandra Eder, Günther Daum, Fritz Paltauf, Felix Wieland, Sepp D. Kohlwein
出版事項 1999Artigo -
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Cell-specific deletion of glucosylceramide synthase in brain leads to severe neural defects after birth 著者: Richard Jennemann, Roger Sandhoff, Shijun Wang, Éva Kiss, Norbert Gretz, Cecilia Zuliani, Ana Martín-Villalba, Richard Jäger, Hubert Schorle, Marc Kenzelmann, Mahnaz Bonrouhi, Herbert Wiegandt, Hermann-Josef Gröne
出版事項 2005Artigo -
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Sulfatides are required for renal adaptation to chronic metabolic acidosis 著者: Paula Stettner, Soline Bourgeois, Christian Marsching, Milena Traykova-Brauch, Štefan Porubský, Viola Nordström, Carsten Hopf, Robert Koesters, Roger Sandhoff, Herbert Wiegandt, Carsten A. Wagner, Hermann‐Josef Gröne, Richard Jennemann
出版事項 2013Artigo
関連主題
Biology
Biochemistry
Cell biology
Gene
Sphingolipid
Apoptosis
Ceramide
Chemistry
Endocrinology
Genetics
Medicine
Enzyme
Mutant
Immunology
Inflammation
Internal medicine
Membrane
Central nervous system
Ceramide synthase
Ganglioside
Anatomy
Disease
Endoplasmic reticulum
Glycolipid
In vitro
Barrier function
Cerebellum
Epidermis (zoology)
Germ cell
Golgi apparatus