Risultati della ricerca - Roger Sandhoff
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Very long chain sphingolipids: Tissue expression, function and synthesis di Roger Sandhoff
Pubblicazione 2009Revisão -
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Emerging concepts of ganglioside metabolism di Roger Sandhoff, Konrad Sandhoff
Pubblicazione 2018Revisão -
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Adult Ceramide Synthase 2 (CERS2)-deficient Mice Exhibit Myelin Sheath Defects, Cerebellar Degeneration, and Hepatocarcinomas di Silke Imgrund, Dieter Hartmann, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Volkmar Gieselmann, Konrad Sandhoff, Klaus Willecke
Pubblicazione 2009Artigo -
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Depletion of ceramides with very long chain fatty acids causes defective skin permeability barrier function, and neonatal lethality in ELOVL4 deficient mice di Wenmei Li, Roger Sandhoff, Mari Kono, Patricia M. Zerfas, Vickie Hoffmann, Bryan Char-Hoa Ding, Richard L. Proia, Chu‐Xia Deng
Pubblicazione 2007Artigo -
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Diastereomer-specific quantification of bioactive hexosylceramides from bacteria and mammals di Johanna von Gerichten, Kerstin Schlosser, Dominic Lamprecht, Ivan Morace, Matthias Eckhardt, Dagmar Wachten, Richard Jennemann, Hermann-Josef Gröne, Matthias Mack, Roger Sandhoff
Pubblicazione 2017Artigo -
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Interruption of ganglioside synthesis produces central nervous system degeneration and altered axon–glial interactions di Tadashi Yamashita, Yunping Wu, Roger Sandhoff, Norbert Werth, Hiroki Mizukami, Jessica M. Ellis, Jeffrey L. Dupree, Rudolf Geyer, Konrad Sandhoff, Richard L. Proia
Pubblicazione 2005Artigo -
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Male meiotic cytokinesis requires ceramide synthase 3-dependent sphingolipids with unique membrane anchors di Mariona Rabionet, Aline Bayerle, Richard Jennemann, Hans Heid, Jens Fuchser, Christian Marsching, Štefan Porubský, Christian Bolenz, Florian Guillou, Hermann‐Josef Gröne, Karin Gorgas, Roger Sandhoff
Pubblicazione 2015Artigo -
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Ablation of Neuronal Ceramide Synthase 1 in Mice Decreases Ganglioside Levels and Expression of Myelin-associated Glycoprotein in Oligodendrocytes di Christina Ginkel, Dieter Hartmann, Katharina vom Dorp, Armin Zlomuzica, Hany Farwanah, Matthias Eckhardt, Roger Sandhoff, Joachim Degen, Mariona Rabionet, Ekrem Dere, Peter Dörmann, Konrad Sandhoff, Klaus Willecke
Pubblicazione 2012Artigo -
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Electrospray Ionization Tandem Mass Spectrometry (Esi-Ms/Ms) Analysis of the Lipid Molecular Species Composition of Yeast Subcellular Membranes Reveals Acyl Chain-Based Sorting/Rem... di Roger Schneiter, Britta Brügger, Roger Sandhoff, Günther Zellnig, A. Philip Leber, Manfred Lampl, Karin Athenstaedt, Claudia Hrastnik, Sandra Eder, Günther Daum, Fritz Paltauf, Felix Wieland, Sepp D. Kohlwein
Pubblicazione 1999Artigo -
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Cell-specific deletion of glucosylceramide synthase in brain leads to severe neural defects after birth di Richard Jennemann, Roger Sandhoff, Shijun Wang, Éva Kiss, Norbert Gretz, Cecilia Zuliani, Ana Martín-Villalba, Richard Jäger, Hubert Schorle, Marc Kenzelmann, Mahnaz Bonrouhi, Herbert Wiegandt, Hermann-Josef Gröne
Pubblicazione 2005Artigo -
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Novel Class of Glycosphingolipids Involved in Male Fertility di Roger Sandhoff, Rudolf Geyer, Richard Jennemann, Claudia Paret, Éva Kiss, Tadashi Yamashita, Karin Gorgas, Tjeerd Sijmonsma, Masao Iwamori, C. Finaz, Richard L. Proia, Herbert Wiegandt, Hermann-Josef Gröne
Pubblicazione 2005Artigo -
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Sulfatides are required for renal adaptation to chronic metabolic acidosis di Paula Stettner, Soline Bourgeois, Christian Marsching, Milena Traykova-Brauch, Štefan Porubský, Viola Nordström, Carsten Hopf, Robert Koesters, Roger Sandhoff, Herbert Wiegandt, Carsten A. Wagner, Hermann‐Josef Gröne, Richard Jennemann
Pubblicazione 2013Artigo
Strumenti per la ricerca:
Soggetti correlati
Biology
Biochemistry
Cell biology
Gene
Sphingolipid
Apoptosis
Ceramide
Chemistry
Endocrinology
Genetics
Medicine
Enzyme
Mutant
Immunology
Inflammation
Internal medicine
Membrane
Central nervous system
Ceramide synthase
Ganglioside
Anatomy
Disease
Endoplasmic reticulum
Glycolipid
In vitro
Barrier function
Cerebellum
Epidermis (zoology)
Germ cell
Golgi apparatus