检索结果 - Paolo Scudieri
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TRPV4 and purinergic receptor signalling pathways are separately linked in airway epithelia to CFTR and TMEM16A chloride channels 由 Michele Genovese, Anna Borrelli, Arianna Venturini, Daniela Guidone, Emanuela Caci, Gaetano Viscido, Gennaro Gambardella, Diego di Bernardo, Paolo Scudieri, Luis J. V. Galietta
出版 2019Artigo -
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Ionocytes and CFTR Chloride Channel Expression in Normal and Cystic Fibrosis Nasal and Bronchial Epithelial Cells 由 Paolo Scudieri, Ilaria Musante, Arianna Venturini, Daniela Guidone, Michele Genovese, Federico Cresta, Emanuela Caci, A. Palleschi, Marco Poeta, Francesca Santamaria, Fabiana Ciciriello, V. Lucidi, Luis J. V. Galietta
出版 2020Artigo -
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Association of TMEM16A chloride channel overexpression with airway goblet cell metaplasia 由 Paolo Scudieri, Emanuela Caci, Silvia Bruno, Loretta Ferrera, Marco Schiavon, Elvira Sondo, Valeria Tomati, Ambra Gianotti, Olga Zegarra‐Moran, Nicoletta Pedemonte, Federico Rea, Roberto Ravazzolo, Luis J. V. Galietta
出版 2012Artigo -
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Increased expression of ATP12A proton pump in cystic fibrosis airways 由 Paolo Scudieri, Ilaria Musante, Emanuela Caci, Arianna Venturini, Patrizia Morelli, Christine Walter, Davide Tosi, A. Palleschi, Pablo Martı́n-Vasallo, Isabelle Sermet‐Gaudelus, Gabrielle Planelles, Gilles Crambert, Luis J. V. Galietta
出版 2018Artigo -
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Discovery of a picomolar potency pharmacological corrector of the mutant CFTR chloride channel 由 Nicoletta Pedemonte, Fabio Bertozzi, Emanuela Caci, Federico Sorana, Paolo Di Fruscia, Valeria Tomati, Loretta Ferrera, A. Rodríguez-Gimeno, Francesco Berti, Emanuela Pesce, Elvira Sondo, Ambra Gianotti, Paolo Scudieri, Tiziano Bandiera, Luis J. V. Galietta
出版 2020Artigo -
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Two CFTR mutations within codon 970 differently impact on the chloride channel functionality 由 Felice Amato, Paolo Scudieri, Ilaria Musante, Valeria Tomati, Emanuela Caci, Marika Comegna, Sabrina Maietta, Francesca Manzoni, Antonella Miriam Di Lullo, Elke De Wachter, Eef Vanderhelst, Vito Terlizzi, C. Braggion, Giuseppe Castaldo, Luis J. V. Galietta
出版 2019Artigo -
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Goblet Cell Hyperplasia Requires High Bicarbonate Transport To Support Mucin Release 由 Giulia Gorrieri, Paolo Scudieri, Emanuela Caci, Marco Schiavon, Valeria Tomati, Francesco Sirci, Francesco Napolitano, Diego Carrella, Ambra Gianotti, Ilaria Musante, Maria Favia, Valeria Casavola, Lorenzo Guerra, Federico Rea, Roberto Ravazzolo, Diego di Bernardo, Luis J. V. Galietta
出版 2016Artigo -
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Light‐responsive microRNA miR‐211 targets Ezrin to modulate lysosomal biogenesis and retinal cell clearance 由 Federica Naso, Daniela Intartaglia, Danila Falanga, Chiara Soldati, Elena Polishchuk, Giuliana Giamundo, Paola Tiberi, Elena Marrocco, Paolo Scudieri, Chiara Di Malta, Ivana Trapani, Edoardo Nusco, Francesco Giuseppe Salierno, Enrico Maria Surace, Luis J. V. Galietta, Sandro Banfi, Alberto Auricchio, Andrea Ballabio, Diego L. Medina, Iván Conte
出版 2020Artigo -
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Genotype-Phenotype Correlations in Neurofibromatosis Type 1: A Single-Center Cohort Study 由 Marcello Scala, Irene Schiavetti, Francesca Madia, Cristina Chelleri, Gianluca Piccolo, Andrea Accogli, Antonella Riva, Vincenzo Salpietro, Renata Bocciardi, Guido Morcaldi, Marco Di Duca, Francesco Caroli, Antonio Verrico, Claudia Milanaccio, Gianmaria Viglizzo, Monica Traverso, Sımona Baldassari, Paolo Scudieri, Michele Iacomino, Gianluca Piatelli, Carlo Minetti, Pasquale Striano, Maria Luisa Garrè, Patrizia De Marco, Maria Cristina Diana, Valeria Capra, Marco Pavanello, Federico Zara
出版 2021Artigo -
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Epilepsy Course and Developmental Trajectories in <i>STXBP1</i> -DEE 由 Ganna Balagura, Julie Xian, Antonella Riva, Francesca Marchese, Bruria Ben Zeev, Loreto Ríos, Deepa Sirsi, Patrizia Accorsi, Elisabetta Amadori, Guja Astrea, Sımona Baldassari, Francesca Beccaria, Antonella Boni, M Budetta, Gaetano Cantalupo, Giuseppe Capovilla, Elisabetta Cesaroni, Valentina Chiesa, Antonietta Coppola, Robertino Dilena, Raffaella Faggioli, Anna Rita Ferrari, Elena Fiorini, Francesca Madia, Elena Di Gennaro, Thea Giacomini, Lucio Giordano, Michele Iacomino, Simona Lattanzi, Carla Marini, Maria Margherita Mancardi, Massimo Mastrangelo, Tullio Messana, Carlo Minetti, Lino Nobili, Amanda Papa, Antonia Parmeggiani, Tiziana Pisano, Angelo Russo, Vincenzo Salpietro, Salvatore Savasta, Marcello Scala, Andrea Accogli, Barbara Scelsa, Paolo Scudieri, Alberto Spalice, Nicola Specchio, Marina Trivisano, Michal Tzadok, Massimiliano Valeriani, Maria Stella Vari, Alberto Verrotti, Federico Vigevano, Aglaia Vignoli, Ruud F. Toonen, Federico Zara, Ingo Helbig, Pasquale Striano
出版 2022Artigo
相关主题
Biology
Biochemistry
Gene
Cell biology
Chemistry
Medicine
Chloride channel
Cystic fibrosis
Genetics
Cystic fibrosis transmembrane conductance regulator
Endocrinology
Epithelium
Internal medicine
Secretion
Ecology
Mucus
Pathology
Respiratory epithelium
Bicarbonate
Biophysics
Cell
Downregulation and upregulation
Epilepsy
In vitro
Intracellular
Membrane
Missense mutation
Molecular biology
Mutant
Mutation