檢索結果 - Osamu Onodera
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Transglutaminase-catalyzed inactivation of glyceraldehyde 3-phosphate dehydrogenase and α-ketoglutarate dehydrogenase complex by polyglutamine domains of pathological length 由 Arthur J.L. Cooper, K.‐F. R. Sheu, James R. Burke, Osamu Onodera, Warren J. Strittmatter, Allen D. Roses, John P. Blass
出版 1997Artigo -
9
Aprataxin, causative gene product for EAOH/AOA1, repairs DNA single-strand breaks with damaged 3′-phosphate and 3′-phosphoglycolate ends 由 Tetsuya Takahashi, Masayoshi Tada, Shuichi Igarashi, Akihide Koyama, Hidetoshi Date, Akio Yokoseki, Atsushi Shiga, Yutaka Yoshida, Shoji Tsuji, Masatoyo Nishizawa, Osamu Onodera
出版 2007Artigo -
10
Microglia preconditioned by oxygen-glucose deprivation promote functional recovery in ischemic rats 由 Masato Kanazawa, Minami Miura, Masafumi Toriyabe, Misaki Koyama, Masahiro Hatakeyama, Masanori Ishikawa, Takashi Nakajima, Osamu Onodera, Tetsuya Takahashi, Masatoyo Nishizawa, Takayoshi Shimohata
出版 2017Artigo -
11
Phosphorylated TDP-43 aggregates in skeletal and cardiac muscle are a marker of myogenic degeneration in amyotrophic lateral sclerosis and various conditions 由 Fumiaki Mori, Mari Tada, Tomoya Kon, Yasuo Miki, Kunikazu Tanji, Hidekachi Kurotaki, Masahiko Tomiyama, Tomohiko Ishihara, Osamu Onodera, Akiyoshi Kakita, Koichi Wakabayashi
出版 2019Artigo -
12
Clinical and genetic characterization of adult‐onset leukoencephalopathy with axonal spheroids and pigmented glia associated with <i><scp>CSF</scp>1R</i> mutation 由 Takuya Konno, Kunihiro Yoshida, Toshiki Mizuno, Toshitaka Kawarai, Masayoshi Tada, Hiroaki Nozaki, Shu‐ichi Ikeda, Masatoyo Nishizawa, Osamu Onodera, Z. Wszolek, Takeshi Ikeuchi
出版 2016Artigo -
13
Elevated C-Reactive Protein Is Associated with Cognitive Decline in Outpatients of a General Hospital: The Project in Sado for Total Health (PROST) 由 Yumi Watanabe, Kaori Kitamura, Kazutoshi Nakamura, Kazuhiro Sanpei, Minako Wakasugi, Akio Yokoseki, Osamu Onodera, Takeshi Ikeuchi, Ryozo Kuwano, Takeshi Momotsu, Ichiei Narita, Naoto Endo
出版 2016Artigo -
14
Evidence that phosphorylated ubiquitin signaling is involved in the etiology of Parkinson’s disease 由 Kahori Shiba‐Fukushima, Kei‐ichi Ishikawa, Tsuyoshi Inoshita, Nana Izawa, Masashi Takanashi, Shigeto Sato, Osamu Onodera, Wado Akamatsu, Hideyuki Okano, Yuzuru Imai, Nobutaka Hattori
出版 2017Artigo -
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Diagnostic criteria for adult‐onset leukoencephalopathy with axonal spheroids and pigmented glia due to <i><scp>CSF</scp>1R</i> mutation 由 Takuya Konno, K. Yoshida, Ikuko Mizuta, Toshiki Mizuno, Toshitaka Kawarai, Mari Tada, Hiroaki Nozaki, Shu‐ichi Ikeda, Osamu Onodera, Zbigniew K. Wszołek, Takeshi Ikeuchi
出版 2017Artigo -
16
Increased cytoplasmic<i>TARDBP</i>mRNA in affected spinal motor neurons in ALS caused by abnormal autoregulation of TDP-43 由 Akihide Koyama, Akihiro Sugai, Taisuke Kato, Tomohiko Ishihara, Atsushi Shiga, Yasuko Toyoshima, Misaki Koyama, Takuya Konno, Sachiko Hirokawa, Akio Yokoseki, Masatoyo Nishizawa, Akiyoshi Kakita, Hitoshi Takahashi, Osamu Onodera
出版 2016Artigo -
17
Alteration of POLDIP3 Splicing Associated with Loss of Function of TDP-43 in Tissues Affected with ALS 由 Atsushi Shiga, Tomohiko Ishihara, Akinori Miyashita, Misaki Kuwabara, Taisuke Kato, Norihiro Watanabe, Akie Yamahira, Chigusa Kondo, Akio Yokoseki, Masuhiro Takahashi, Ryozo Kuwano, Akiyoshi Kakita, Masatoyo Nishizawa, Hitoshi Takahashi, Osamu Onodera
出版 2012Artigo -
18
Heterogeneity of cerebral TDP-43 pathology in sporadic amyotrophic lateral sclerosis: Evidence for clinico-pathologic subtypes 由 Ryoko Takeuchi, Mari Tada, Atsushi Shiga, Yasuko Toyoshima, Takuya Konno, Tomoe Sato, Hiroaki Nozaki, Taisuke Kato, Masao Horie, Hiroshi Shimizu, Hirohide Takebayashi, Osamu Onodera, Masatoyo Nishizawa, Akiyoshi Kakita, Hitoshi Takahashi
出版 2016Artigo -
19
Decreased number of Gemini of coiled bodies and U12 snRNA level in amyotrophic lateral sclerosis 由 Tomohiko Ishihara, Yuko Ariizumi, Atsushi Shiga, Taisuke Kato, Chun-Feng Tan, Tatsuya Sato, Yukari Miki, Mariko Yokoo, Takeshi Fujino, Akihide Koyama, Akio Yokoseki, Masatoyo Nishizawa, Akiyoshi Kakita, Hitoshi Takahashi, Osamu Onodera
出版 2013Artigo -
20
Clinical, molecular and histopathological features of short stature syndrome with novel CUL7 mutation in Yakuts: new population isolate in Asia 由 Н. Р. Максимова, Kenju Hara, A Miyashia, И. В. Николаева, Atsushi Shiga, Anna Nogovicina, A. L. Sukhomyasova, V. A. Argunov, Anna A. Shvedova, Takeshi Ikeuchi, Masatoyo Nishizawa, Ryozo Kuwano, Osamu Onodera
出版 2007Artigo
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