نتائج البحث - Melissa McAlonis‐Downes
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C1q induction and global complement pathway activation do not contribute to ALS toxicity in mutant SOD1 mice حسب Christian S. Lobsiger, Séverine Boillée, Christine D. Pozniak, Amir M. Khan, Melissa McAlonis‐Downes, Joseph W. Lewcock, Don W. Cleveland
منشور في 2013Artigo -
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Enhancing Mitochondrial Calcium Buffering Capacity Reduces Aggregation of Misfolded SOD1 and Motor Neuron Cell Death without Extending Survival in Mouse Models of Inherited Amyotro... حسب Philippe A. Parone, Sandrine Da Cruz, Joo Seok Han, Melissa McAlonis‐Downes, Anne P. Vetto, Sandra K. Lee, Eva Tseng, Don W. Cleveland
منشور في 2013Artigo -
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Mutant SOD1 in cell types other than motor neurons and oligodendrocytes accelerates onset of disease in ALS mice حسب Koji Yamanaka, Séverine Boillée, Elizabeth A. Roberts, Michael L. Garcia, Melissa McAlonis‐Downes, Oliver R. Mikse, Don W. Cleveland, Lawrence S.B. Goldstein
منشور في 2008Artigo -
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Misfolded SOD1 Associated with Motor Neuron Mitochondria Alters Mitochondrial Shape and Distribution Prior to Clinical Onset حسب Christine Vande Velde, Karli K. McDonald, Yasmin Boukhedimi, Melissa McAlonis‐Downes, Christian S. Lobsiger, Samar Bel Hadj, Andre Zandona, Jean‐Pierre Julien, Sameer B. Shah, Don W. Cleveland
منشور في 2011Artigo -
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Mutant TDP-43 within motor neurons drives disease onset but not progression in amyotrophic lateral sclerosis حسب Dara Ditsworth, Marcus Maldonado, Melissa McAlonis‐Downes, Shuying Sun, Amanda Seelman, Kevin Drenner, Eveline S. Arnold, Shuo‐Chien Ling, Donald Pizzo, John Ravits, Don W. Cleveland, Sandrine Da Cruz
منشور في 2017Artigo -
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Therapeutically viable generation of neurons with antisense oligonucleotide suppression of PTB حسب Roy Maimon, Carlos Chillón-Marinas, Cedric E. Snethlage, Sarthak M. Singhal, Melissa McAlonis‐Downes, Karen Ling, Frank Rigo, C. Frank Bennett, Sandrine Da Cruz, Thomas S. Hnasko, Alysson R. Muotri, Don W. Cleveland
منشور في 2021Artigo -
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Translational profiling identifies a cascade of damage initiated in motor neurons and spreading to glia in mutant SOD1-mediated ALS حسب Shuying Sun, Ying Sun, Shuo‐Chien Ling, Laura Ferraiuolo, Melissa McAlonis‐Downes, Yiyang Zou, Kevin Drenner, Yin Wang, Dara Ditsworth, Seiya Tokunaga, Alex Kopelevich, Brian K. Kaspar, Clotilde Lagier‐Tourenne, Don W. Cleveland
منشور في 2015Artigo -
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Elevated PGC-1α Activity Sustains Mitochondrial Biogenesis and Muscle Function without Extending Survival in a Mouse Model of Inherited ALS حسب Sandrine Da Cruz, Philippe A. Parone, Vanda S. Lopes, Concepción Lillo, Melissa McAlonis‐Downes, Sandra K. Lee, Anne P. Vetto, Susanna Petrosyan, Martin Maršala, Anne N. Murphy, David S. Williams, Bruce M. Spiegelman, Don W. Cleveland
منشور في 2012Artigo -
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Macrophage Migration Inhibitory Factor as a Chaperone Inhibiting Accumulation of Misfolded SOD1 حسب Adrian Israelson, Dara Ditsworth, Shuying Sun, SungWon Song, Jason Liang, Marián Hruška-Plocháň, Melissa McAlonis‐Downes, Salah Abu‐Hamad, Guy Zoltsman, Tom Shani, Marcus Maldonado, Anh Thu Bui, Michael Navarro, Huilin Zhou, Martin Maršala, Brian K. Kaspar, Sandrine Da Cruz, Don W. Cleveland
منشور في 2015Artigo -
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ALS-linked TDP-43 mutations produce aberrant RNA splicing and adult-onset motor neuron disease without aggregation or loss of nuclear TDP-43 حسب Eveline S. Arnold, Shuo‐Chien Ling, Stephanie C. Huelga, Clotilde Lagier‐Tourenne, Magdalini Polymenidou, Dara Ditsworth, Holly Kordasiewicz, Melissa McAlonis‐Downes, Oleksandr Platoshyn, Philippe A. Parone, Sandrine Da Cruz, Kevin M. Clutario, Debbie Swing, Lino Tessarollo, Martin Maršala, Christopher E. Shaw, G Yeo, Don W. Cleveland
منشور في 2013Artigo -
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Reduced C9ORF72 function exacerbates gain of toxicity from ALS/FTD-causing repeat expansion in C9orf72 حسب Qiang Zhu, Jie Jiang, Tania F. Gendron, Melissa McAlonis‐Downes, Lu-Lin Jiang, Amy E. Taylor, Sandra Diaz Garcia, Somasish Ghosh Dastidar, Maria José Gómez-Rodríguez, Patrick King, Yong‐Jie Zhang, Albert R. La Spada, Huaxi Xu, Leonard Petrucelli, John Ravits, Sandrine Da Cruz, Clotilde Lagier‐Tourenne, Don W. Cleveland
منشور في 2020Artigo -
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Spinal subpial delivery of AAV9 enables widespread gene silencing and blocks motoneuron degeneration in ALS حسب Mariana Bravo‐Hernández, Takahiro Tadokoro, Michael Navarro, Oleksandr Platoshyn, Yoshiomi Kobayashi, Silvia Marsala, Atsushi Miyanohara, Štefan Juhás, Jana Juhásová, Helena Kupcová Skalníková, Z Tomori, Ivo Vanický, Hana Studenovská, Vladimír Proks, Peixi Chen, Noé Govea-Perez, Dara Ditsworth, Joseph D. Ciacci, Shang Gao, Wenlian Zhu, Eric T. Ahrens, Shawn P. Driscoll, Thomas D. Glenn, Melissa McAlonis‐Downes, Sandrine Da Cruz, Samuel L. Pfaff, Brian K. Kaspar, Don W. Cleveland, Martin Maršala
منشور في 2019Artigo -
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Stathmin-2 loss leads to neurofilament-dependent axonal collapse driving motor and sensory denervation حسب Jone López‐Erauskin, Mariana Bravo‐Hernández, Maximiliano Presa, Michael W. Baughn, Ze’ev Melamed, Melinda S. Beccari, Ana Rita Agra de Almeida Quadros, Olatz Arnold-García, Aamir Zuberi, Karen Ling, Oleksandr Platoshyn, Elkin Niño-Jara, I. Sandra Ndayambaje, Melissa McAlonis‐Downes, Larissa Cabrera, Jonathan W. Artates, Jennifer Ryan, Anita Hermann, John Ravits, C. Frank Bennett, Paymaan Jafar‐Nejad, Frank Rigo, Martin Maršala, Cathleen Lutz, Don W. Cleveland, Clotilde Lagier‐Tourenne
منشور في 2023Artigo -
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Targeted degradation of sense and antisense <i>C9orf72</i> RNA foci as therapy for ALS and frontotemporal degeneration حسب Clotilde Lagier‐Tourenne, Michael W. Baughn, Frank Rigo, Shuying Sun, Patrick Liu, Hairi Li, Jie Jiang, Andrew T. Watt, Seung Chun, Melanie Katz, Jinsong Qiu, Ying Sun, Shuo‐Chien Ling, Qiang Zhu, Magdalini Polymenidou, Kevin Drenner, Jonathan W. Artates, Melissa McAlonis‐Downes, Sebastian Markmiller, Kasey R. Hutt, Donald Pizzo, Janet Cady, Matthew B. Harms, Robert H. Baloh, Scott R. VandenBerg, G Yeo, Xiang‐Dong Fu, C. Frank Bennett, Don W. Cleveland, John Ravits
منشور في 2013Artigo -
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ALS/FTD-Linked Mutation in FUS Suppresses Intra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS حسب Jone López‐Erauskin, Takahiro Tadokoro, Michael W. Baughn, Brian E. Myers, Melissa McAlonis‐Downes, Carlos Chillón-Marinas, Joshua N. Asiaban, Jonathan W. Artates, Anh Thu Bui, Anne P. Vetto, Sandra K. Lee, Ai Vy Le, Ying Sun, Mélanie Jambeau, Jihane Boubaker, Deborah A. Swing, Jinsong Qiu, Geoffrey G. Hicks, Zhengyu Ouyang, Xiang‐Dong Fu, Lino Tessarollo, Shuo‐Chien Ling, Philippe A. Parone, Christopher E. Shaw, Martin Maršala, Clotilde Lagier‐Tourenne, Don W. Cleveland, Sandrine Da Cruz
منشور في 2018Artigo -
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Overriding FUS autoregulation in mice triggers gain-of-toxic dysfunctions in RNA metabolism and autophagy-lysosome axis حسب Shuo‐Chien Ling, Somasish Ghosh Dastidar, Seiya Tokunaga, Wan Yun Ho, Kenneth Teck Kiat Lim, Hristelina Ilieva, Philippe A. Parone, Sheue-Houy Tyan, Tsemay M. Tse, Jer-Cherng Chang, Oleksandr Platoshyn, Ngoc B Bui, Anh Thu Bui, Anne P. Vetto, Shuying Sun, Melissa McAlonis‐Downes, Joo Seok Han, Debbie Swing, Katannya Kapeli, G Yeo, Lino Tessarollo, Martin Maršala, Christopher E. Shaw, Greg Tucker‐Kellogg, Albert R. La Spada, Clotilde Lagier‐Tourenne, Sandrine Da Cruz, Don W. Cleveland
منشور في 2019Artigo -
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Gain of Toxicity from ALS/FTD-Linked Repeat Expansions in C9ORF72 Is Alleviated by Antisense Oligonucleotides Targeting GGGGCC-Containing RNAs حسب Jie Jiang, Qiang Zhu, Tania F. Gendron, Shahram Saberi, Melissa McAlonis‐Downes, Amanda Seelman, Jennifer E. Stauffer, Paymaan Jafar‐Nejad, Kevin Drenner, Derek Schulte, Seung Chun, Shuying Sun, Shuo‐Chien Ling, Brian Myers, Jeffery A. Engelhardt, Melanie Katz, Michael W. Baughn, Oleksandr Platoshyn, Martin Maršala, Andy Watt, Charles J. Heyser, M. Colin Ard, Louis De Muynck, Lillian M. Daughrity, Deborah A. Swing, Lino Tessarollo, Chris Jung, Arnaud Delpoux, Daniel T. Utzschneider, Stephen Μ. Hedrick, Pieter J. de Jong, Dieter Edbauer, Philip Van Damme, Leonard Petrucelli, Christopher E. Shaw, C. Frank Bennett, Sandrine Da Cruz, John Ravits, Frank Rigo, Don W. Cleveland, Clotilde Lagier‐Tourenne
منشور في 2016Artigo
أدوات البحث:
موضوعات ذات صلة
Biology
Disease
Medicine
Gene
Amyotrophic lateral sclerosis
Cell biology
Neuroscience
Pathology
Genetics
SOD1
Biochemistry
Mutant
Motor neuron
Spinal cord
Internal medicine
Immunology
Neurodegeneration
Central nervous system
Dementia
Frontotemporal dementia
Mitochondrion
RNA
Anatomy
Apoptosis
C9orf72
Chemistry
Oxidative stress
Superoxide dismutase
Allele
Autophagy