Хайлтын үр дүнгүүд - Joseph R. Mazzulli
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Is Parkinson’s disease a lysosomal disorder? -н Andrés D. Klein, Joseph R. Mazzulli
Хэвлэсэн 2018Artigo -
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Rescue of α-synuclein aggregation in Parkinson’s patient neurons by synergistic enhancement of ER proteostasis and protein trafficking -н Iva Stojkovska, Willayat Yousuf Wani, Friederike Zunke, Nandkishore R. Belur, Egor Pavlenko, Nkatha Mwenda, Karan Sharma, Laetitia Francelle, Joseph R. Mazzulli
Хэвлэсэн 2021Artigo -
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Cytosolic Catechols Inhibit α-Synuclein Aggregation and Facilitate the Formation of Intracellular Soluble Oligomeric Intermediates -н Joseph R. Mazzulli, Amanda J. Mishizen, Benoit I. Giasson, David R. Lynch, Steven Thomas, Akira Nakashima, Toshiharu Nagatsu, Akira Ota, Harry Ischiropoulos
Хэвлэсэн 2006Artigo -
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Distinct Region-Specific α-Synuclein Oligomers in A53T Transgenic Mice: Implications for Neurodegeneration -н Elpida Tsika, Maria Moysidou, Jing Guo, Mimi Cushman, Patrick J. Gannon, Raphael Sandaltzopoulos, Benoit I. Giasson, Dimitri Krainc, Harry Ischiropoulos, Joseph R. Mazzulli
Хэвлэсэн 2010Artigo -
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Characterization of the complex formed by β-glucocerebrosidase and the lysosomal integral membrane protein type-2 -н Friederike Zunke, Lisa Andresen, Sophia Wesseler, Johann Groth, Philipp Arnold, Michelle Rothaug, Joseph R. Mazzulli, Dimitri Krainc, Judith Blanz, Paul Säftig, Michael Schwake
Хэвлэсэн 2016Artigo -
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Reversible Conformational Conversion of α-Synuclein into Toxic Assemblies by Glucosylceramide -н Friederike Zunke, Alexandra C. Moise, Nandkishore R. Belur, Eilrayna Gelyana, Iva Stojkovska, Haris Dzaferbegovic, Nicholas Toker, Sohee Jeon, Kristina Fredriksen, Joseph R. Mazzulli
Хэвлэсэн 2017Artigo -
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Sirt1 mediates neuroprotection from mutant huntingtin by activation of the TORC1 and CREB transcriptional pathway -н Hyunkyung Jeong, Dena E. Cohen, Libin Cui, Andrea Supinski, Jeffrey N. Savas, Joseph R. Mazzulli, John R. Yates, Laura Bordone, Leonard Guarente, Dimitri Krainc
Хэвлэсэн 2011Artigo -
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Gaucher Disease Glucocerebrosidase and α-Synuclein Form a Bidirectional Pathogenic Loop in Synucleinopathies -н Joseph R. Mazzulli, You-Hai Xu, Ying Sun, Adam L. Knight, Pamela J. McLean, Guy A. Caldwell, Ellen Sidransky, Gregory A. Grabowski, Dimitri Krainc
Хэвлэсэн 2011Artigo -
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Activation of -Glucocerebrosidase Reduces Pathological -Synuclein and Restores Lysosomal Function in Parkinson's Patient Midbrain Neurons -н Joseph R. Mazzulli, Friederike Zunke, Taiji Tsunemi, Nicholas Toker, Sohee Jeon, Lena F. Burbulla, Samarjit Patnaik, Ellen Sidransky, Juan Marugán, Carolyn M. Sue, Dimitri Krainc
Хэвлэсэн 2016Artigo -
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Acetylation Targets Mutant Huntingtin to Autophagosomes for Degradation -н Hyunkyung Jeong, Florian Then, Thomas J. Melia, Joseph R. Mazzulli, Libin Cui, Jeffrey N. Savas, Cindy Voisine, Paolo Paganetti, Naoko Tanese, Anne C. Hart, Ai Yamamoto, Dimitri Krainc
Хэвлэсэн 2009Artigo -
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Reciprocal effects of alpha-synuclein aggregation and lysosomal homeostasis in synucleinopathy models -н Alice Drobny, Fanni Annamária Boros, Denise Balta, Susy Prieto Huarcaya, Deniz Caylioglu, Niyeti Qazi, Julia Vandrey, Yanni Schneider, Jan Philipp Dobert, Caleb Pitcairn, Joseph R. Mazzulli, Friederike Zunke
Хэвлэсэн 2023Artigo -
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Increased Lysosomal Exocytosis Induced by Lysosomal Ca<sup>2+</sup> Channel Agonists Protects Human Dopaminergic Neurons from α-Synuclein Toxicity -н Taiji Tsunemi, Tamara Perez‐Rosello, Yuta Ishiguro, Asako Yoroisaka, Sohee Jeon, Kana Hamada, Malini Rammonhan, Yvette C. Wong, Zhong Xie, Wado Akamatsu, Joseph R. Mazzulli, D. James Surmeier, Nobutaka Hattori, Dimitri Krainc
Хэвлэсэн 2019Artigo -
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Parkin and PINK1 Patient iPSC-Derived Midbrain Dopamine Neurons Exhibit Mitochondrial Dysfunction and α-Synuclein Accumulation -н Sun Young Chung, Sarah Kishinevsky, Joseph R. Mazzulli, John J. Graziotto, Ana Mrejeru, Eugene V. Mosharov, Lesly Puspita, Parvin Valiulahi, David Sulzer, Teresa A. Milner, Tony Taldone, Dimitri Krainc, Lorenz Studer, Jae-won Shim
Хэвлэсэн 2016Artigo
Хайх хэрэгслүүд:
Холбогдох сэдвүүд
Biology
Medicine
Disease
Cell biology
Parkinson's disease
Biochemistry
Gene
Neuroscience
Alpha-synuclein
Internal medicine
Pathology
Chemistry
Neurodegeneration
Genetics
Apoptosis
Dopamine
Enzyme
Autophagy
Protein aggregation
Dopaminergic
Synucleinopathies
Embryonic stem cell
Induced pluripotent stem cell
Bioinformatics
Fibril
Glucocerebrosidase
Intracellular
Mutant
Biophysics
Central nervous system