检索结果 - Herbst, Ruth
- Showing 1 - 18 results of 18
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Neuromuscular synapse integrity requires linkage of acetylcholine receptors to postsynaptic intermediate filament networks via rapsyn–plectin 1f complexes 由 Mihailovska, Eva, Raith, Marianne, Valencia, Rocio G., Fischer, Irmgard, Banchaabouchi, Mumna Al, Herbst, Ruth, Wiche, Gerhard
出版 2014Text -
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Essential role of B-Raf in oligodendrocyte maturation and myelination during postnatal central nervous system development 由 Galabova-Kovacs, Gergana, Catalanotti, Federica, Matzen, Dana, Reyes, Gloria X., Zezula, Jürgen, Herbst, Ruth, Silva, Alcino, Walter, Ingrid, Baccarini, Manuela
出版 2008Text -
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Rescuing Z(+) agrin splicing in Nova null mice restores synapse formation and unmasks a physiologic defect in motor neuron firing 由 Ruggiu, Matteo, Herbst, Ruth, Kim, Natalie, Jevsek, Marko, Fak, John J., Mann, Mary Anne, Fischbach, Gerald, Burden, Steven J., Darnell, Robert B.
出版 2009Text -
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Congenital myasthenic syndrome due to mutations in MUSK suggests that the level of MuSK phosphorylation is crucial for governing synaptic structure 由 Rodríguez Cruz, Pedro M., Cossins, Judith, Cheung, Jonathan, Maxwell, Susan, Jayawant, Sandeep, Herbst, Ruth, Waithe, Dominic, Kornev, Alexandr P., Palace, Jacqueline, Beeson, David
出版 2019Text -
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Reduced muscle strength in ether lipid‐deficient mice is accompanied by altered development and function of the neuromuscular junction 由 Dorninger, Fabian, Herbst, Ruth, Kravic, Bojana, Camurdanoglu, Bahar Z., Macinkovic, Igor, Zeitler, Gerhard, Forss‐Petter, Sonja, Strack, Siegfried, Khan, Muzamil Majid, Waterham, Hans R., Rudolf, Rüdiger, Hashemolhosseini, Said, Berger, Johannes
出版 2017Text -
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A Mutation Causes MuSK Reduced Sensitivity to Agrin and Congenital Myasthenia 由 Ben Ammar, Asma, Soltanzadeh, Payam, Bauché, Stéphanie, Richard, Pascale, Goillot, Evelyne, Herbst, Ruth, Gaudon, Karen, Huzé, Caroline, Schaeffer, Laurent, Yamanashi, Yuji, Higuchi, Osamu, Taly, Antoine, Koenig, Jeanine, Leroy, Jean-Paul, Hentati, Fayçal, Najmabadi, Hossein, Kahrizi, Kimia, Ilkhani, Manouchehr, Fardeau, Michel, Eymard, Bruno, Hantaï, Daniel
出版 2013Text -
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Correction: A Mutation Causes MuSK Reduced Sensitivity to Agrin and Congenital Myasthenia 由 Ben Ammar, Asma, Soltanzadeh, Payam, Bauché, Stéphanie, Richard, Pascale, Goillot, Evelyne, Herbst, Ruth, Gaudon, Karen, Huzé, Caroline, Schaeffer, Laurent, Yamanashi, Yuji, Higuchi, Osamu, Taly, Antoine, Koenig, Jeanine, Leroy, Jean-Paul, Hentati, Fayçal, Najmabadi, Hossein, Kahrizi, Kimia, Ilkhani, Manouchehr, Fardeau, Michel, Eymard, Bruno, Hantaï, Daniel
出版 2013Text -
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The RNA kinase CLP1 links tRNA metabolism to progressive motor neuron loss 由 Hanada, Toshikatsu, Weitzer, Stefan, Mair, Barbara, Bernreuther, Christian, Wainger, Brian J., Ichida, Justin, Hanada, Reiko, Orthofer, Michael, Cronin, Shane J, Komnenovic, Vukislav, Minis, Adi, Sato, Fuminori, Mimata, Hiromitsu, Yoshimura, Akihiko, Tamir, Ido, Rainer, Johannes, Kofler, Reinhard, Yaron, Avraham, Eggan, Kevin C., Woolf, Clifford J., Glatzel, Markus, Herbst, Ruth, Martinez, Javier, Penninger, Josef M.
出版 2013Text