Ngā hua rapu - Han‐Xiang Deng
- E whakaatu ana i te 1 - 20 hua o te 33
- Haere ki te Whārangi Whai Ake
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Genetics of amyotrophic lateral sclerosis mā Teepu Siddique, Han‐Xiang Deng
I whakaputaina 1996Revisão -
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Hyperactive Intracellular Calcium Signaling Associated with Localized Mitochondrial Defects in Skeletal Muscle of an Animal Model of Amyotrophic Lateral Sclerosis mā Jingsong Zhou, Jianxun Yi, Ronggen Fu, Erdong Liu, Teepu Siddique, Eduardo Rı́os, Han‐Xiang Deng
I whakaputaina 2009Artigo -
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Intense Superoxide Dismutase-1 Immunoreactivity in Intracytoplasmic Hyaline Inclusions of Familial Amyotrophic Lateral Sclerosis with Posterior Column Involvement mā Noriyuki Shibata, Asao Hirano, Makio Kobayashi, Teepu Siddique, Han‐Xiang Deng, Wu-Yen Hung, Takeo Kato, Kohtaro Asayama
I whakaputaina 1996Artigo -
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Molecular dissection of ALS-associated toxicity of SOD1 in transgenic mice using an exon-fusion approach mā Han-Xiang, Deng, Hujun, Jiang, Ronggen, Fu, Hong, Zhai, Yong, Shi, Erdong, Liu, Makito, Hirano, Mauro, C. Dal Canto, Teepu, Siddique
I whakaputaina 2008Text -
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Marked accumulation of 27-hydroxycholesterol in SPG5 patients with hereditary spastic paresis mā Rebecca Schüle, Teepu Siddique, Han‐Xiang Deng, Yi Yang, Sandra Donkervoort, Magnus Hansson, R. E. Madrid, Nailah Siddique, Lüdger Schöls, Ingemar Björkhem
I whakaputaina 2009Artigo -
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Nuclear export of misfolded SOD1 mediated by a normally buried NES-like sequence reduces proteotoxicity in the nucleus mā Yongwang Zhong, Jiou Wang, Mark J. Henderson, Peixin Yang, Brian M. Hagen, Teepu Siddique, Bruce E. Vogel, Han‐Xiang Deng, Shengyun Fang
I whakaputaina 2017Artigo -
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TDP-43 pathology in primary progressive aphasia and frontotemporal dementia with pathologic Alzheimer disease mā Eileen H. Bigio, Manjari Mishra, Kimmo J. Hatanpaa, Charles L. White, Nancy Johnson, Alfred Rademaker, Bing Bing Weitner, Han‐Xiang Deng, Steven Dubner, Sandra Weıntraub, Marsel Mesulam
I whakaputaina 2010Artigo -
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Inclusions in frontotemporal lobar degeneration with TDP-43 proteinopathy (FTLD-TDP) and amyotrophic lateral sclerosis (ALS), but not FTLD with FUS proteinopathy (FTLD-FUS), have p... mā Eileen H. Bigio, Jane Y. Wu, Han‐Xiang Deng, Esther N. Bit‐Ivan, Qinwen Mao, Rakhee Ganti, Melanie Peterson, Nailah Siddique, Changiz Geula, Teepu Siddique, Marsel Mesulam
I whakaputaina 2013Carta -
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Mutation in the novel nuclear-encoded mitochondrial protein CHCHD10 in a family with autosomal dominant mitochondrial myopathy mā Senda Ajroud‐Driss, Faisal Fecto, Kaouther Ajroud, Irfan Lalani, Sarah E. Calvo, Vamsi K. Mootha, Han‐Xiang Deng, Nailah Siddique, Albert J. Tahmoush, Terry Heiman‐Patterson, Teepu Siddique
I whakaputaina 2014Artigo -
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FUS‐immunoreactive inclusions are a common feature in sporadic and non‐SOD1 familial amyotrophic lateral sclerosis mā Han‐Xiang Deng, Hong Zhai, Eileen H. Bigio, Jianhua Yan, Faisal Fecto, Kaouther Ajroud, Manjari Mishra, Senda Ajroud‐Driss, Scott Heller, Robert Sufit, Nailah Siddique, Enrico Mugnaini, Teepu Siddique
I whakaputaina 2010Artigo
Ngā utauta rapu:
Ngā marau whai pānga
Biology
Gene
Medicine
Genetics
Disease
Pathology
Amyotrophic lateral sclerosis
Mutation
SOD1
Biochemistry
Cell biology
Internal medicine
Dementia
Frontotemporal dementia
Mutant
Chemistry
Neuroscience
Transgene
Frontotemporal lobar degeneration
Genetically modified mouse
Mitochondrion
Molecular biology
Oxidative stress
C9orf72
Endocrinology
Phenotype
Neurodegeneration
Protein aggregation
Superoxide dismutase
Allele