Rezultati - Dominique Debray
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Gallbladder and bile duct disease in Cystic Fibrosis od David N. Assis, Dominique Debray
Izdano 2017Revisão -
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Cystic fibrosis-related liver disease: Clinical presentations, diagnostic and monitoring approaches in the era of CFTR modulator therapies od Jérémy Dana, Dominique Debray, Aurélie Beaufrère, Sophie Hillaire, Monique Fabrè, Caroline Reinhold, Thomas F. Baumert, Laureline Berteloot, Valérie Vilgrain
Izdano 2021Revisão -
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Towards a Standardized Classification of the Hepatobiliary Manifestations in Cystic Fibrosis (CFHBI): A Joint ESPGHAN/NASPGHAN Position Paper od Frank A.J.A. Bodewes, A. Jay Freeman, Alexander Weymann, Dominique Debray, Isabelle Scheers, Henkjan J. Verkade, Michael R. Narkewicz
Izdano 2024Artigo -
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The Long-Term Outcome of Hepatic Artery Thrombosis After Liver Transplantation in Children: Role of Urgent Revascularization od O. Ackermann, Sophie Branchereau, Stéphanie Franchi‐Abella, D. Pariente, L. Chevret, Dominique Debray, Emmanuel Jacquemin, Frédéric Gauthier, Catherine Hill, Olivier Bernard
Izdano 2012Artigo -
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Defects in Gallbladder Emptying and Bile Acid Homeostasis in Mice With Cystic Fibrosis Transmembrane Conductance Regulator Deficiencies od Dominique Debray, Dominique Rainteau, Véronique Barbu, Myriam Rouahi, Haquima El Mourabit, Stéphanie Lerondel, Colette Rey, Lydie Humbert, Dominique Wendum, Charles‐Henry Cottart, Paul A. Dawson, Nicolas Chignard, Chantal Housset
Izdano 2012Artigo -
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Diagnosis and Management of Pediatric Autoimmune Liver Disease od Giorgina Mieli‐Vergani, Diego Vergani, Ulrich Baumann, Piotr Czubkowski, Dominique Debray, Antal Dezsöfi, Björn Fischler, Girish Gupte, Loreto Hierro, Giuseppe Indolfi, Jörg Jahnel, Françoise Smets, Henkjan J. Verkade, Nedim Hadžić
Izdano 2017Revisão -
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Treatment of Chronic Hepatitis C Virus Infection in Children od Giuseppe Indolfi, Loreto Hierro, Antal Dezsöfi, Jörg Jahnel, Dominique Debray, Nedim Hadžić, Piotr Czubkowski, Girish Gupte, Yael Mozer‐Glassberg, Wendy van der Woerd, Françoise Smets, Henkjan J. Verkade, Björn Fischler
Izdano 2017Artigo -
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Lumacaftor-ivacaftor effects on cystic fibrosis-related liver involvement in adolescents with homozygous F508 del-CFTR od David Drummond, Jérémy Dana, Laureline Berteloot, Elena K. Schneider‐Futschik, F. Chedevergne, Céline Bailly-Botuha, Thao Nguyen‐Khoa, Mathieu Cornet, M. Le Bourgeois, Dominique Debray, M Girard, Isabelle Sermet‐Gaudelus
Izdano 2021Artigo -
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MYO5B and bile salt export pump contribute to cholestatic liver disorder in microvillous inclusion disease od M Girard, Florence Lacaille, Virginie Verkarre, Raphaël Matégot, Gérard Feldmann, Alain Grodet, Frédérique Sauvat, Sabine Irtan, Anne Davit–Spraul, Emmanuel Jacquemin, Frank M. Ruemmele, Dominique Rainteau, Olivier Goulet, V. Colomb, Christophe Chardot, Alexandra Henrion‐Caude, Dominique Debray
Izdano 2013Artigo -
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Prognosis of Children Undergoing Liver Transplantation: A 30-Year European Study od Ulrich Baumann, Vincent Karam, René Adam, Constantino Fondevila, Anil Dhawan, Étienne Sokal, Emmanuel Jacquemin, Déirdre Kelly, Enke Grabhorn, Joanna Pawłowska, Lorenzo D’Antiga, Paloma Jara, Dominique Debray, Wojciech G. Polak, Jean de Ville de Goyet, Henkjan J. Verkade
Izdano 2022Editorial -
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The Health Care Transition of Youth With Liver Disease Into the Adult Health System od Pietro Vajro, Björn Fischler, Patrizia Burra, Dominique Debray, Antal Dezsöfi, Salvatore Guercio Nuzio, Nedim Hadzic, Loreto Hierro, J. Jahnel, Thierry Lamireau, Patrick McKiernan, Valérie A. McLin, Valerio Nobili, Piotr Socha, Françoise Smets, Ulli Baumann, Henkjan J. Verkade
Izdano 2018Artigo -
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Long-term outcome of pediatric liver transplantation for biliary atresia: A 10-year follow-up in a single center od Virginie Fouquet, Arnaud Alvès, Sophie Branchereau, Sophie Grabar, Dominique Debray, Emmanuel Jacquemin, Denis Devictor, Philippe Durand, Catherine Baujard, Monique Fabrè, D. Pariente, Christophe Chardot, B. Dousset, Pierre‐Philippe Massault, Denis Bernard, D Houssin, Olivier Bernard, Fr�d�ric Gauthier, Olivier Soubrane
Izdano 2005Artigo
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Gene
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Biliary atresia
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Cystic fibrosis transmembrane conductance regulator
Genetics
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