Výsledky vyhledávání - Darius Ebrahimi‐Fakhari
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Molecular Chaperones and Co-Chaperones in Parkinson Disease Autor Hemi Dimant, Darius Ebrahimi‐Fakhari, Pamela J. McLean
Vydáno 2012Revisão -
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Alpha-synuclein’s degradation in vivo Autor Darius Ebrahimi‐Fakhari, Pamela J. McLean, Vivek K. Unni
Vydáno 2012Artigo -
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Distinct Roles<i>In Vivo</i>for the Ubiquitin–Proteasome System and the Autophagy–Lysosomal Pathway in the Degradation of α-Synuclein Autor Darius Ebrahimi‐Fakhari, Ippolita Cantuti‐Castelvetri, Zhanyun Fan, Edward Rockenstein, Eliezer Masliah, Bradley T. Hyman, Pamela J. McLean, Vivek K. Unni
Vydáno 2011Artigo -
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The Stress-Induced Atf3-Gelsolin Cascade Underlies Dendritic Spine Deficits in Neuronal Models of Tuberous Sclerosis Complex Autor Duyu Nie, Zehua Chen, Darius Ebrahimi‐Fakhari, Alessia Di Nardo, Kristina Jülich, Victoria Robson, Yuan Cheng, Clifford J. Woolf, Maxwell G. Heiman, Mustafa Şahin
Vydáno 2015Artigo -
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Reduction of TMEM97 increases NPC1 protein levels and restores cholesterol trafficking in Niemann-pick type C1 disease cells Autor Darius Ebrahimi‐Fakhari, Lara Wahlster, Fabian Bartz, Jennifer Werenbeck-Ueding, Maria Praggastis, Jessie Zhang, Brigitte Joggerst-Thomalla, Susanne Theiß, Dirk Grimm, Daniel S. Ory, Heiko Runz
Vydáno 2016Artigo -
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The Circadian Protein BMAL1 Regulates Translation in Response to S6K1-Mediated Phosphorylation Autor Jonathan O. Lipton, Elizabeth D. Yuan, Lara M. Boyle, Darius Ebrahimi‐Fakhari, Erica Kwiatkowski, Ashwin Nathan, Thomas Güttler, Fred C. Davis, John M. Asara, Mustafa Şahin
Vydáno 2015Artigo -
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Alpha-synuclein aggregation involves a bafilomycin A<sub>1</sub>-sensitive autophagy pathway Autor Jochen Klucken, Anne-Maria Poehler, Darius Ebrahimi‐Fakhari, Jacqueline Schneider, Silke Nuber, Edward Rockenstein, Ursula Schlötzer‐Schrehardt, Bradley T. Hyman, Pamela J. McLean, Eliezer Masliah, Jürgen Winkler
Vydáno 2012Artigo -
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Incidence of tuberous sclerosis and age at first diagnosis: new data and emerging trends from a national, prospective surveillance study Autor Daniel Ebrahimi‐Fakhari, Lilian Lisa Mann, Martin Poryo, Norbert Graf, Rüdiger von Kries, B. Heinrich, Darius Ebrahimi‐Fakhari, Marina Flotats‐Bastardas, Ludwig Gortner, Michael Zemlin, Sascha Meyer
Vydáno 2018Artigo -
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AP-4-mediated axonal transport controls endocannabinoid production in neurons Autor Alexandra K. Davies, Julian E. Alecu, M. L. ZIEGLER, Catherine G. Vasilopoulou, Fabrizio Merciai, Hellen Jumo, Wardiya Afshar Saber, Mustafa Şahin, Darius Ebrahimi‐Fakhari, Georg H. H. Borner
Vydáno 2022Artigo -
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Intrathecal AAV9/AP4M1 gene therapy for hereditary spastic paraplegia 50 shows safety and efficacy in preclinical studies Autor Xin Chen, Thomas Dong, Yuhui Hu, Raffaella De Pace, Rafael Mattera, Kathrin Eberhardt, M. L. ZIEGLER, Terry Pirovolakis, Mustafa Şahin, Juan S. Bonifacino, Darius Ebrahimi‐Fakhari, Steven J. Gray
Vydáno 2023Artigo -
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Impaired Mitochondrial Dynamics and Mitophagy in Neuronal Models of Tuberous Sclerosis Complex Autor Darius Ebrahimi‐Fakhari, Afshin Saffari, Lara Wahlster, Alessia Di Nardo, Daria Turner, Tommy L. Lewis, Christopher Conrad, Jonathan M. Rothberg, Jonathan O. Lipton, Stefan Kölker, Georg F. Hoffmann, Min‐Joon Han, Franck Polleux, Mustafa Şahin
Vydáno 2016Errata/Corrigenda -
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AAV gene therapy for hereditary spastic paraplegia type 50: a phase 1 trial in a single patient Autor James J. Dowling, Terry Pirovolakis, Keshini Devakandan, Ana Stosic, Mia Pidsadny, Elisa Nigro, Mustafa Şahin, Darius Ebrahimi‐Fakhari, Souad Messahel, G. S. Varadarajan, Benjamin Greenberg, Xin Chen, Berge A. Minassian, Ronald D. Cohn, Carsten G. Bönnemann, Steven J. Gray
Vydáno 2024Artigo -
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Nomenclature of Genetic Movement Disorders: Recommendations of the International Parkinson and Movement Disorder Society Task Force – An Update Autor Lara M. Lange, Paulina González-Latapí, Rajasumi Rajalingam, Marina A.J. Tijssen, Darius Ebrahimi‐Fakhari, Carolin Gabbert, Christos Ganos, Rhia Ghosh, Kishore R. Kumar, Anthony E. Lang, Malco Rossi, Sterre van der Veen, Bart P.C. van de Warrenburg, Thomas T. Warner, Katja Lohmann, Christine Klein, Connie Marras
Vydáno 2022Revisão
Vyhledávací nástroje:
Související témata
Biology
Medicine
Gene
Genetics
Cell biology
Disease
Neuroscience
Pathology
Apoptosis
Autophagy
Biochemistry
Internal medicine
Parkinson's disease
Alpha-synuclein
Pediatrics
Phenotype
Endoplasmic reticulum
Hereditary spastic paraplegia
Neurodegeneration
Proteasome
Protein aggregation
Bioinformatics
Protein degradation
Psychiatry
Signal transduction
In vivo
PI3K/AKT/mTOR pathway
Proteostasis
Unfolded protein response
Aggresome