Хайлтын үр дүнгүүд - Daniel J.M. Fernández‐Ayala
- 10-н 1 - 10 үр дүнгүүдийг харуулж байна
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Mitochondrial ROS Produced via Reverse Electron Transport Extend Animal Lifespan -н Filippo Scialò, Ashwin Sriram, Daniel J.M. Fernández‐Ayala, Nina Gubina, Madis Lõhmus, Glyn Nelson, Angela Logan, Helen Cooper, Plácido Navas, José Antonio Enrı́quez, Michael P. Murphy, Alberto Sanz
Хэвлэсэн 2016Artigo -
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Expression of the Ciona intestinalis Alternative Oxidase (AOX) in Drosophila Complements Defects in Mitochondrial Oxidative Phosphorylation -н Daniel J.M. Fernández‐Ayala, Alberto Sanz, Suvi Vartiainen, Kia K. Kemppainen, Marek Babušiak, Eero Mustalahti, Rodolfo Costa, Tea Tuomela, Massimo Zeviani, Jongkyeong Chung, Kevin M.C. O’Dell, Pierre Rustin, Howard T. Jacobs
Хэвлэсэн 2009Artigo -
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Mutations of GEMIN5 are associated with coenzyme Q10 deficiency: long-term follow-up after treatment -н Marivi V. Cascajo-Almenara, Natalia Juliá‐Palacios, Roser Urreizti, Ana Sánchez‐Cuesta, Daniel J.M. Fernández‐Ayala, Elena García-Díaz, Clara Oliva, Maria del Mar O ́Callaghan, Abraham J. Paredes‐Fuentes, Pedro Moreno, Jordi Muchart, A. Nascimento, C. Ortez, Daniel Natera‐de Benito, M. Pineda, Noelia Rivera, Tyler R. Fortuna, Deepa Rajan, Plácido Navas, Leonardo Salviati, Francesc Palau, Dèlia Yubero, Àngels García‐Cazorla, Udai Bhan Pandey, Carlos Santos–Ocaña, Rafael Artuch
Хэвлэсэн 2024Artigo -
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ADCK2 Haploinsufficiency Reduces Mitochondrial Lipid Oxidation and Causes Myopathy Associated with CoQ Deficiency -н Luis Vázquez-Fonseca, J. Schaefer, Ignacio Navas‐Enamorado, Carlos Santos–Ocaña, Juan Diego Hernández‐Camacho, Ignacio Guerra, María V. Cascajo, Ana Sánchez‐Cuesta, Zoltán Horváth, Emilio Siendones, Cristina Jou, Mercedes Casado, Purificacion Gutierrez-Ríos, Gloria Brea‐Calvo, Guillermo López‐Lluch, Daniel J.M. Fernández‐Ayala, Ana Cortés, Juan Carlos Rodríguez‐Aguilera, Cristiane Matté, Antònia Ribes, S Prieto, Eduardo Domínguez‐del‐Toro, Andrea Di Francesco, Miguel A. Aon, Michel Bernier, Leonardo Salviati, Rafael Artuch, Rafael de Cabo, Sandra L. Jackson, Plácido Navas
Хэвлэсэн 2019Artigo -
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ADCK2 Haploinsufficiency Reduces Mitochondrial Lipid Oxidation and Causes Myopathy Associated with CoQ Deficiency -н Luis Vázquez-Fonseca, Jochen Schäfer, Ignacio Navas‐Enamorado, Carlos Santos–Ocaña, Juan Diego Hernández‐Camacho, Ignacio Guerra, María V. Cascajo, Ana Sánchez‐Cuesta, Zoltán Horváth, Emilio Siendones, Cristina Jou, Mercedes Casado, Purificacion Gutierrez-Ríos, Gloria Brea‐Calvo, Guillermo López‐Lluch, Daniel J.M. Fernández‐Ayala, Ana Belén Cortés-Rodríguez, Juan Carlos Rodríguez‐Aguilera, Cristiane Matté, Antònia Ribes, S Prieto, Eduardo Domínguez‐del‐Toro, Andrea Di Francesco, Miguel A. Aon, Michel Bernier, Leonardo Salviati, Rafael Artuch, Rafael de Cabo, Sandra L. Jackson, Plácido Navas
Хэвлэсэн 2019Pré-impressão
Хайх хэрэгслүүд:
Холбогдох сэдвүүд
Biology
Gene
Mitochondrion
Biochemistry
Internal medicine
Medicine
Cell biology
Genetics
Mitochondrial DNA
Phenotype
Coenzyme Q10
Drosophila melanogaster
Endocrinology
Mitochondrial ROS
Mitochondrial disease
Reactive oxygen species
Beta oxidation
Fatty acid metabolism
Gene expression
Gene knockdown
Haploinsufficiency
Insulin
Insulin resistance
Lipid metabolism
Lipotoxicity
Mitochondrial myopathy
Myopathy
Oxidative phosphorylation
Oxidative stress
Skeletal muscle