نتائج البحث - Chen, Jeng‐Haur
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Human cystic fibrosis airway epithelia have reduced Cl(−) conductance but not increased Na(+) conductance حسب Itani, Omar A., Chen, Jeng-Haur, Karp, Philip H., Ernst, Sarah, Keshavjee, Shaf, Parekh, Kalpaj, Klesney-Tait, Julia, Zabner, Joseph, Welsh, Michael J.
منشور في 2011نص -
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Inhibition of Protein Kinase CK2 Closes the CFTR Cl(−) Channel, but has no Effect on the Cystic Fibrosis Mutant ΔF508-CFTR حسب Treharne, Kate J., Xu, Zhe, Chen, Jeng-Haur, Best, O. Giles, Cassidy, Diane M., Gruenert, Dieter C., Hegyi, Péter, Gray, Michael A., Sheppard, David N., Kunzelmann, Karl, Mehta, Anil
منشور في 2009نص -
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Protein kinase CK2, cystic fibrosis transmembrane conductance regulator, and the ΔF508 mutation. F508 deletion disrupts a kinase-binding site. VOLUME 282 (2007) PAGES 10804-10813 حسب Treharne, Kate J., Crawford, Russell M., Xu, Zhe, Chen, Jeng-Haur, Best, O. Giles, Schulte, Eva A., Gruenert, Dieter C., Wilson, Stuart M., Sheppard, David N., Kunzelmann, Kar, Mehta, Anil
منشور في 2008نص -
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CFTR-deficient pigs display peripheral nervous system defects at birth حسب Reznikov, Leah R., Dong, Qian, Chen, Jeng-Haur, Moninger, Thomas O., Park, Jung Min, Zhang, Yuzhou, Du, Jianyang, Hildebrand, Michael S., Smith, Richard J. H., Randak, Christoph O., Stoltz, David A., Welsh, Michael J.
منشور في 2013نص -
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Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia حسب Chen, Jeng-Haur, Stoltz, David A., Karp, Philip H., Ernst, Sarah E., Pezzulo, Alejandro A., Moninger, Thomas O., Rector, Michael V., Reznikov, Leah R., Launspach, Janice L., Chaloner, Kathryn, Zabner, Joseph, Welsh, Michael J.
منشور في 2010نص -
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CFTR founder mutation causes protein trafficking defects in Chinese patients with cystic fibrosis حسب Leung, Gordon K. C., Ying, Dingge, Mak, Christopher C. Y., Chen, Xin‐Ying, Xu, Weiyi, Yeung, Kit‐San, Wong, Wai‐Lap, Chu, Yoyo W. Y., Mok, Gary T. K., Chau, Christy S. K., McLuskey, Jenna, Ong, Winnie P. T., Leong, Huey‐Yin, Chan, Kelvin Y. K., Yang, Wanling, Chen, Jeng‐Haur, Li, Albert M., Sham, Pak C., Lau, Yu‐Lung, Chung, Brian H. Y., Lee, So‐Lun
منشور في 2016نص -
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The ΔF508 Mutation Causes CFTR Misprocessing and Cystic Fibrosis-Like Disease in Pigs حسب Ostedgaard, Lynda S, Meyerholz, David K, Chen, Jeng-Haur, Pezzulo, Alejandro A, Karp, Philip H, Rokhlina, Tatiana, Ernst, Sarah E, Hanfland, Robert A, Reznikov, Leah R, Ludwig, Paula S, Rogan, Mark P, Davis, Greg J, Dohrn, Cassie L, Wohlford-Lenane, Christine, Taft, Peter J, Rector, Michael V, Hornick, Emma, Nassar, Boulos S, Samuel, Melissa, Zhang, Yuping, Richter, Sandra S, Uc, Aliye, Shilyansky, Joel, Prather, Randall S, McCray, Paul B, Zabner, Joseph, Welsh, Michael J, Stoltz, David A
منشور في 2011نص -
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Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs حسب Stoltz, David A., Rokhlina, Tatiana, Ernst, Sarah E., Pezzulo, Alejandro A., Ostedgaard, Lynda S., Karp, Philip H., Samuel, Melissa S., Reznikov, Leah R., Rector, Michael V., Gansemer, Nicholas D., Bouzek, Drake C., Alaiwa, Mahmoud H. Abou, Hoegger, Mark J., Ludwig, Paula S., Taft, Peter J., Wallen, Tanner J., Wohlford-Lenane, Christine, McMenimen, James D., Chen, Jeng-Haur, Bogan, Katrina L., Adam, Ryan J., Hornick, Emma E., Nelson, George A., Hoffman, Eric A., Chang, Eugene H., Zabner, Joseph, McCray, Paul B., Prather, Randall S., Meyerholz, David K., Welsh, Michael J.
منشور في 2013نص