Risultati della ricerca - Cécile Debacker
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Heptahelical protein PQLC2 is a lysosomal cationic amino acid exporter underlying the action of cysteamine in cystinosis therapy di Adrien Jézégou, Elisa Llinares, Christine Anne, Sylvie Kieffer‐Jaquinod, S O’Regan, Joëlle Aupetit, A. Chabli, Corinne Sagné, Cécile Debacker, Bernadette Chadefaux-Vekemans, Agnès Journet, Bruno André, Bruno Gasnier
Pubblicazione 2012Artigo -
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Expression and lysosomal targeting of CLN7, a major facilitator superfamily transporter associated with variant late-infantile neuronal ceroid lipofuscinosis di Azita Sharifi, Maria Kousi, Corinne Sagné, Gian Carlo Bellenchi, Lydie Morel, Michèle Darmon, Helena Hůlková, Raquel Ruivo, Cécile Debacker, Salah El Mestikawy, M. Elleder, Anna‐Elina Lehesjoki, Anu Jalanko, Bruno Gasnier, Aija Kyttälä
Pubblicazione 2010Artigo -
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MFSD1 with its accessory subunit GLMP functions as a general dipeptide uniporter in lysosomes di Katharina E. J. Jungnickel, Océane Guelle, Miharu Iguchi, Wentao Dong, Vadim Kotov, Florian Gabriel, Cécile Debacker, Julien Dairou, Isabelle McCort‐Tranchepain, Nouf N. Laqtom, Sze Ham Chan, Akika Ejima, Kenji Sato, David Massa López, Paul Säftig, Ahmad Reza Mehdipour, Monther Abu-Remaileh, Bruno Gasnier, Christian Löw, Markus Daμμe
Pubblicazione 2024Artigo
Strumenti per la ricerca:
Soggetti correlati
Biology
Gene
Biochemistry
Cell biology
Chemistry
Enzyme
Transport protein
Cysteine
Cystine
Major facilitator superfamily
Membrane
Transporter
Bacteriorhodopsin
Biophysics
Cerebellum
Cysteamine
Cystinosis
Cytosol
Disease
Electrochemical gradient
Genetics
Ion
Medicine
Membrane potential
Membrane protein
Mutant
Neurodegeneration
Neuronal ceroid lipofuscinosis
Neuroscience
Organic chemistry