Výsledky vyhledávání - Benoît Florkin
- Zobrazuji výsledky 1 - 12 z 12
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Anakinra pharmacokinetics in children and adolescents with systemic-onset juvenile idiopathic arthritis and autoinflammatory syndromes Autor Saı̈k Urien, Christophe Bardin, Brigitte Bader‐Meunier, Richard Mouy, Sandrine Compeyrot‐Lacassagne, Frantz Foissac, Benoît Florkin, Carine Wouters, Bénédicte Neven, Jean‐Marc Tréluyer, Pierre Quartier
Vydáno 2013Artigo -
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Cernunnos Deficiency Reduces Thymocyte Life Span and Alters the T Cell Repertoire in Mice and Humans Autor Gabriella Vera, Paola Rivera-Muñoz, Vincent Abramowski, Laurent Malivert, Apiradee Lim, Christine Bôle‐Feysot, Christelle Martin, Benoît Florkin, Sylvain Latour, Patrick Revy, Jean‐Pierre de Villartay
Vydáno 2012Artigo -
4
Treatment of severe forms of LPS-responsive beige-like anchor protein deficiency with allogeneic hematopoietic stem cell transplantation Autor Markus G. Seidel, K. Böhm, Figen Doğu, Austen Worth, Adrian J. Thrasher, Benoît Florkin, Aydan İkincioğulları, Anke Peters, Shahrzad Bakhtiar, Marie Meeths, Polina Stepensky, Isabelle Meyts, Svetlana O. Sharapova, Laura Gámez‐Díaz, Lennart Hammarström, Stephan Ehl, Bodo Grimbacher, Andrew R. Gennery
Vydáno 2017Carta -
5
A survey of 90 patients with autoimmune lymphoproliferative syndrome related to TNFRSF6 mutation Autor Bénédicte Neven, Aude Magérus‐Chatinet, Benoît Florkin, Delphine Gobert, Olivier Lambotte, Lien De Somer, Nina Lanzarotti, Marie–Claude Stolzenberg, Brigitte Bader‐Meunier, Nathalie Aladjidi, Christophe Chantrain, Yves Bertrand, Éric Jeziorski, Guy Leverger, Gérard Michel, Felipe Suárez, Éric Oksenhendler, Olivier Hermine, Stéphane Blanche, Capucine Pïcard, Alain Fischer, Frédéric Rieux‐Laucat
Vydáno 2011Artigo -
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Defective anti-polysaccharide response and splenic marginal zone disorganization in ALPS patients Autor Bénédicte Neven, Julie Bruneau, Marie–Claude Stolzenberg, Isabelle Meyts, Aude Magérus‐Chatinet, Leen Moens, Nina Lanzarotti, Sandra Weller, Denise Amiranoff, Benoît Florkin, Brigitte Bader‐Meunier, Guy Leverger, A Ferster, Christophe Chantrain, Stéphane Blanche, Capucine Pïcard, Thierry Jo Molina, Nicole Brousse, Anne Durandy, Marta Rizzi, Xavier Bossuyt, Alain Fischer, Frédéric Rieux‐Laucat
Vydáno 2014Artigo -
7
Clinical characteristics and outcomes of childhood-onset ANCA-associated vasculitis: a French nationwide study Autor Anne‐Sylvia Sacri, T. Chambaraud, Bruno Ranchin, Benoît Florkin, H. See, Stéphane Decramer, Hugues Flodrops, Tim Ulinski, Emma Allain‐Launay, Olivia Boyer, Olivier Dunand, Michel Fischbach, É. Hachulla, Christine Piétrement, P. Le Pogamp, JL Stéphan, Alexandre Bélot, Hubert Nivet, François Nobili, Loı̈c Guillevin, Pierre Quartier, Georges Deschênes, Rémi Salomon, Marie Essig, J. Harambat
Vydáno 2015Artigo -
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FAS-L, IL-10, and double-negative CD4−CD8− TCR α/β+ T cells are reliable markers of autoimmune lymphoproliferative syndrome (ALPS) associated with FAS loss of function Autor Aude Magérus‐Chatinet, Marie–Claude Stolzenberg, Maria S. Loffredo, Bénédicte Neven, Catherine Schaffner, Nicolas Ducrot, Peter D. Arkwright, Brigitte Bader‐Meunier, José Barbot, Stéphane Blanche, Jean‐Laurent Casanova, Marianne Debré, Alina Ferster, Claire Fieschi, Benoît Florkin, Claire Galambrun, Olivier Hermine, Olivier Lambotte, Éric Solary, Caroline Thomas, Françoise Le Deist, Capucine Pïcard, Alain Fischer, Frédéric Rieux‐Laucat
Vydáno 2009Artigo -
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A sensitive and scalable microsatellite instability assay to diagnose constitutional mismatch repair deficiency by sequencing of peripheral blood leukocytes Autor Richard Gallon, Barbara Mühlegger, Sören-Sebastian Wenzel, Harsh Sheth, Christine Hayes, Stefan Aretz, Karin Dahan, William D. Foulkes, Christian P. Kratz, Tim Ripperger, Amedeo A. Azizi, Hagit Baris Feldman, Anne‐Laure Chong, Uğur Demırsoy, Benoît Florkin, Thomas Imschweiler, Danuta Januszkiewicz‐Lewandowska, Stephan Lobitz, Michaela Nathrath, Hans-Jürgen Pander, Vanesa Pérez‐Alonso, Claudia Perne, Iman Ragab, Thorsten Rosenbaum, Daniel Rueda, Markus G. Seidel, Manon Suerink, Julia Taeubner, Stefanie Zimmermann, Johannes Zschocke, Gillian M. Borthwick, John Burn, Michael S. Jackson, Mauro Santibanez‐Koref, Katharina Wimmer
Vydáno 2019Artigo -
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Population-based, first-tier genomic newborn screening in the maternity ward Autor François Boemer, Kristine Hovhannesyan, Flávia Piazzon, Frédéric Minner, Myriam Mni, Valérie Jacquemin, Davood Mashhadizadeh, Noor Benmhammed, Vincent Bours, Adeline Jacquinet, Julie Harvengt, Saskia Bulk, Vinciane Dideberg, Laura Helou, Léonor Palmeira, Tamara Dangouloff, Serpil Alkan, Christophe Barrea, Paulina Bartoszek, Émeline Bequet, H. Boboli, Romain Bruninx, Laure Collard, Aurore Daron, François-Guillaume Debray, Marie-Françoise Dresse, Jean-Marie Dubru, Iulia Ebetiuc, Benoît Florkin, Caroline Jacquemart, Céline Kempeneers, Nadège Hennuy, Marie-Christine Lebrethon, Marie Leonard, Patricia Leroy, Angélique Lhomme, Jacques Lombet, Sabine Michotte, Ariane Milet, Anne‐Simone Parent, Vincent Rigo, Marie-Christine Seghaye, Sandrine Vaessen, Laurent Servais
Vydáno 2025Artigo -
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Long-term outcome of LRBA deficiency in 76 patients after various treatment modalities as evaluated by the immune deficiency and dysregulation activity (IDDA) score Autor Victoria K. Tesch, Hassan Abolhassani, Bella Shadur, Joachim Zobel, Yuliya Mareika, Svetlana O. Sharapova, Elif Karakoç-Aydıner, Jacques G. Rivière, Marina García-Prat, Nicolette Moes, Filomeen Haerynck, Luis I. Gonzales-Granado, Juan Luis Santos Pérez, Anna Mukhinа, Anna Shcherbina, Asghar Aghamohammadi, Lennart Hammarström, Figen Doğu, Şule Haskoloğlu, Aydan İkincioğulları, Sevgi Köstel Bal, Safa Barış, Sara Şebnem Kılıç, Neslihan Edeer Karaca, Necil Kütükçüler, Hermann Girschick, Antonios G.A. Kolios, Sevgi Keleş, Vedat Uygun, Polina Stepensky, Austen Worth, Joris M. van Montfrans, Anke Peters, Isabelle Meyts, Mehdi Adeli, Antonio Marzollo, Nurcicek Padem, Amer Khojah, Zahra Chavoshzadeh, Magdalena Avbelj Stefanija, Shahrzad Bakhtiar, Benoît Florkin, Marie Meeths, Laura Gámez‐Díaz, Bodo Grimbacher, Mikko Seppänen, Arjan C. Lankester, Andrew R. Gennery, Markus G. Seidel
Vydáno 2019Artigo -
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TIM3+<i> TRBV11-2</i> T cells and IFNγ signature in patrolling monocytes and CD16+ NK cells delineate MIS-C Autor Levi Hoste, Lisa Roels, Leslie Naesens, Victor Bosteels, Stijn Vanhee, Sam Dupont, Cédric Bosteels, Robin Browaeys, Niels Vandamme, Kevin Verstaen, Jana Roels, Karel Van Damme, Bastiaan Maes, Elisabeth De Leeuw, Jozefien Declercq, Helena Aegerter, Leen Seys, Ursula Smole, Sofie De Prijck, Manon Vanheerswynghels, Karlien Claes, Veronique Debacker, Gert Van Isterdael, Lynn Backers, Kathleen Claes, Paul Bastard, Emmanuelle Jouanguy, Shen‐Ying Zhang, Gilles Mets, Joke Dehoorne, Kristof Vandekerckhove, Petra Schelstraete, Jef Willems, Julie Willekens, Heidi Schaballie, Sabine Van daele, Laure Dierickx, Sara David, Evelyn Dhont, Ann Verrijckt, Annick De Jaeger, Emma Beel, Inge Matthijs, Aurélie Minne, Karin Decaestecker, J Murray John, Thomas E. M. Crijnen, Muriel Koninckx, Joery Verbruggen, Goele Nys, Samira Akhnikh, Koen Vanlede, Annelien Coppens, J. Thijs, Ilse Ryckaert, Annick Covents, E Duval, Ann Verschelde, L. De Keyzer, T Van Ackere, Astrid Verbist, Charlotte Daeze, Caroline Becue, Justine De Paepe, Jo Keepers, Bruno Bruylants, Sabine Kuypers, Siel Daelemans, Jutte van der Werff ten Bosch, Gerlant van Berlaer, Alexandra Dreesman, Benoît Florkin, Cathérine Heijmans, Jean B. Papadopoulos, Patrick Stordeur, Sophie Janssens, Rudi Beyaert, Yvan Saeys, Jean‐Laurent Casanova, Bart N. Lambrecht, Filomeen Haerynck, Simon J. Tavernier
Vydáno 2021Artigo
Vyhledávací nástroje:
Související témata
Biology
Medicine
Immunology
Genetics
Internal medicine
Immune system
Cell biology
Disease
Antibody
Apoptosis
Autoimmune lymphoproliferative syndrome
Biochemistry
CD8
Cancer
Environmental health
Fas receptor
Gene
Genotype
Molecular biology
Pediatrics
Physics
Population
Programmed cell death
Stem cell
T cell
Acoustics
Alkaline phosphatase
Allele
Anakinra
Anti-neutrophil cytoplasmic antibody