检索结果 - Aleksandra Pajak
- Showing 1 - 6 results of 6
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A functional peptidyl-tRNA hydrolase, ICT1, has been recruited into the human mitochondrial ribosome 由 Ricarda Richter, Joanna Rorbach, Aleksandra Pajak, Paul Smith, Hans J. C. T. Wessels, Martijn A. Huynen, Jan Smeitink, Robert N. Lightowlers, Zofia M. Chrzanowska‐Lightowlers
出版 2010Artigo -
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Modulation of mtDNA copy number ameliorates the pathological consequences of a heteroplasmic mtDNA mutation in the mouse 由 Roberta Filograna, Camilla Koolmeister, Mamta Upadhyay, Aleksandra Pajak, Paula Clemente, Rolf Wibom, Marie‐Lune Simard, Anna Wredenberg, Christoph Freyer, James B. Stewart, Nils‐Göran Larsson
出版 2019Artigo -
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C7orf30 specifically associates with the large subunit of the mitochondrial ribosome and is involved in translation 由 Bas F.J. Wanschers, Radek Szklarczyk, Aleksandra Pajak, Mariël A.M. van den Brand, Jolein Gloerich, Richard J. Rodenburg, Robert N. Lightowlers, Leo Nijtmans, Martijn A. Huynen
出版 2012Artigo -
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Defects of mitochondrial RNA turnover lead to the accumulation of double-stranded RNA in vivo 由 Aleksandra Pajak, Isabelle Laine, Paula Clemente, Najla El-Fissi, F. Schober, Camilla Maffezzini, Javier Calvo‐Garrido, Rolf Wibom, Roberta Filograna, Ashish Dhir, Anna Wedell, Christoph Freyer, Anna Wredenberg
出版 2019Artigo -
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Intra-mitochondrial Methylation Deficiency Due to Mutations in SLC25A26 由 Yoshihito Kishita, Aleksandra Pajak, Nikhita Bolar, C Marobbio, Camilla Maffezzini, Daniela Valeria Miniero, Magnus Monné, Masakazu Kohda, Henrik Stranneheim, Kei Murayama, K Naess, Nicole Lesko, Helene Bruhn, Arnaud Mourier, Rolf Wibom, Inger Nennesmo, Ann Jespers, Paul Govaert, Akira Ohtake, Lut Van Laer, Bart Loeys, Christoph Freyer, Ferdinando Palmieri, Anna Wredenberg, Yasushi Okazaki, Anna Wedell
出版 2015Artigo
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Biology
Gene
Genetics
Mitochondrial DNA
RNA
Biochemistry
Messenger RNA
Ribosome
Cell biology
Medicine
Mitochondrial ribosome
Mitochondrion
Molecular biology
Mutation
Translation (biology)
Bacterial protein
Biophysics
Chaperone (clinical)
Chemistry
Co-chaperone
Computational biology
Enzyme
Escherichia coli Proteins
Eukaryotic Large Ribosomal Subunit
Eukaryotic Ribosome
Exosome complex
Heat shock protein
Heteroplasmy
Hsp70
Methylation