نتائج البحث - Al‐Walid Mohsen
- يعرض 1 - 18 نتائج من 18
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Medium branched chain fatty acids improve the profile of tricarboxylic acid cycle intermediates in mitochondrial fatty acid β‐oxidation deficient cells: A comparative study حسب Anuradha Karunanidhi, Clinton Van’t Land, Dhivyaa Rajasundaram, Mateus Grings, Jerry Vockley, Al‐Walid Mohsen
منشور في 2022Artigo -
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ETHE1 and MOCS1 deficiencies: Disruption of mitochondrial bioenergetics, dynamics, redox homeostasis and endoplasmic reticulum-mitochondria crosstalk in patient fibroblasts حسب Mateus Grings, Bianca Seminotti, Anuradha Karunanidhi, Lina Ghaloul‐Gonzalez, Al‐Walid Mohsen, Peter Wipf, Johan Palmfeldt, Jerry Vockley, Guilhian Leipnitz
منشور في 2019Artigo -
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Human Acyl-CoA Dehydrogenase-9 Plays a Novel Role in the Mitochondrial β-Oxidation of Unsaturated Fatty Acids حسب Regina Ensenauer, Miao He, Jan-Marie Willard, Eric S. Goetzman, Thomas J. Corydon, Brian Berg Vandahl, Al‐Walid Mohsen, Grazia Isaya, Jerry Vockley
منشور في 2005Artigo -
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Mitochondrial energetics is impaired in very long-chain acyl-CoA dehydrogenase deficiency and can be rescued by treatment with mitochondria-targeted electron scavengers حسب Bianca Seminotti, Guilhian Leipnitz, Anuradha Karunanidhi, Catherine Kochersperger, Vera Roginskaya, Shrabani Basu, Yu Wang, Peter Wipf, Bennett Van Houten, Al‐Walid Mohsen, Jerry Vockley
منشور في 2018Artigo -
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Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficienc... حسب Guilhian Leipnitz, Al‐Walid Mohsen, Anuradha Karunanidhi, Bianca Seminotti, Vera Roginskaya, Desiree M. Markantone, Mateus Grings, Stephanie J. Mihalik, Peter Wipf, Bennett Van Houten, Jerry Vockley
منشور في 2018Artigo -
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The mitochondrial‐targeted reactive species scavenger <scp>JP4</scp>‐039 prevents sulfite‐induced alterations in antioxidant defenses, energy transfer, and cell death signaling in... حسب Nícolas Manzke Glänzel, Mateus Grings, Nevton Teixeira da Rosa‐Junior, Leila Maria Cereta de Carvalho, Al‐Walid Mohsen, Peter Wipf, Moacır Wajner, Jerry Vockley, Guilhian Leipnitz
منشور في 2020Artigo -
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Outcomes and genotype-phenotype correlations in 52 individuals with VLCAD deficiency diagnosed by NBS and enrolled in the IBEM-IS database حسب Loren Peña, Sandra C. Van Calcar, Joyanna Hansen, Mathew J. Edick, Cate Walsh Vockley, Nancy Leslie, Cynthia A. Cameron, Al‐Walid Mohsen, Susan A. Berry, Georgianne L. Arnold, Jerry Vockley
منشور في 2016Artigo -
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Sirtuin 3 (SIRT3) Protein Regulates Long-chain Acyl-CoA Dehydrogenase by Deacetylating Conserved Lysines Near the Active Site حسب Sivakama S. Bharathi, Yuxun Zhang, Al‐Walid Mohsen, Radha Uppala, Manimalha Balasubramani, Emanuel M. Schreiber, Guy Uechi, Megan E. Beck, Matthew J. Rardin, Jerry Vockley, Eric Verdin, Bradford W. Gibson, Matthew D. Hirschey, Eric S. Goetzman
منشور في 2013Artigo -
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Very long chain fatty acid metabolism is required in acute myeloid leukemia حسب Matthew Tcheng, Alessia Roma, Nawaz Ahmed, Richard Smith, Preethi Jayanth, Mark D. Minden, Aaron D. Schimmer, David A. Hess, Kristin J. Hope, Kevin A. Rea, Tariq A. Akhtar, Eric Bohrnsen, Angelo D’Alessandro, Al‐Walid Mohsen, Jerry Vockley, Paul A. Spagnuolo
منشور في 2021Artigo -
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Mitochondrial bioenergetics and cardiolipin remodeling abnormalities in mitochondrial trifunctional protein deficiency حسب Eduardo Vieira Neto, Meicheng Wang, Austin J. Szuminsky, L. Ferraro, Erik Koppes, Yu Wang, Clinton Van’t Land, Al‐Walid Mohsen, Geancarlo Zanatta, Areeg El‐Gharbawy, Tamil S. Anthonymuthu, Yulia Y. Tyurina, Vladimir A. Tyurin, Valerian E. Kagan, Hülya Bayır, Jerry Vockley
منشور في 2024Artigo -
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Complex I assembly function and fatty acid oxidation enzyme activity of ACAD9 both contribute to disease severity in ACAD9 deficiency حسب Manuel Schiff, Birgit Haberberger, Chuanwu Xia, Al‐Walid Mohsen, Eric S. Goetzman, Yu Wang, Radha Uppala, Yuxun Zhang, Anuradha Karunanidhi, Dolly Prabhu, Hana Alharbi, Edward V. Prochownik, Tobias B. Haack, Johannes Häberle, Arnold Münnich, Agnès Rötig, Robert W. Taylor, Robert D. Nicholls, Jung‐Ja Kim, Holger Prokisch, Jerry Vockley
منشور في 2015Artigo
أدوات البحث:
موضوعات ذات صلة
Biology
Biochemistry
Enzyme
Mitochondrion
Beta oxidation
Chemistry
Gene
Acyl CoA dehydrogenase
Dehydrogenase
Medicine
Bioenergetics
Cell biology
Internal medicine
Oxidative phosphorylation
Fatty acid
Metabolism
Oxidative stress
Fatty acid metabolism
Genetics
Mitochondrial DNA
Mitochondrial disease
Respiratory chain
Citric acid cycle
Coenzyme Q – cytochrome c reductase
Crosstalk
Cytochrome c
Disease
Endocrinology
Endoplasmic reticulum
Long chain fatty acid